following death at 3 1/2 months of age , analysis of the patient 's brain and liver revealed increased amounts of ganglioside gm3 , a virtual absence of higher ganglioside homologues ( gm3 , gm1 , gd1a , and gt1 ) and a deficiency of the biosynthetic enzyme , udp-gal nac : gm3 n-acetylgalactosaminyl-transferase .
C0016897
ganglioside gm3
C0017082
ganglioside