human kidney extracts heated to 60 degrees and devoid of hexosaminidase activity ( 2-acetamido-2-deoxy-beta-d-glucoside acetamidodeoxyglucohydrolase ec 3.2.1.30 ) stimulate more than 20-fold the hexosaminidase a-catalyzed degradation of ganglioside gm2 and of glycolipid ga2 , the neuronal storage compounds of gm2 gangliosidosis .
C0086418
human
C1414471
ga2