an unusual feature of the present case is the florid inflammatory reaction in the adventitia of the aorta , not specifically related to pregnancy or to the marfan syndrome , and it is assumed that in this patient the congenital defect of connective tissue assumed to be the basis of the marfan syndrome is associated with an acute collagen change or necrosis , possibly illustrating a link between the heritable disorders of connective tissue and the diffuse collagen disease .
C0024796
marfan syndrome
C0410787
heritable disorders of connective tissue