the activities of alpha-l-iduronidase ( ec 3.2.1.76 ) were measured , by a microassay with phenyl-alpha-l-iduronide as the substrate , in cultured fibroblasts from patients with the hurler syndrome ( mps ih ) or the scheie syndrome ( mps is ) and from heterozygotes.l the iduronidase activities in the cells from 44 mps ih and 7 mps is patients were all strongly reduced and distinct from the activities in heterozygotes and normal controls .
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fibroblasts
C0007634
the