a family is described in which certain infants presented with a diffuse parenchymal pulmonary disorder characterized by proliferation and desquamation of alveolar epithelial cells that progressed to severe pulmonary fibrosis and cystic dysplasia , resulting in `` '' honeycomb '' '' lung typical of chronic pulmonary interstitial disease ( idiopathic pulmonary fibrosis ) at death .
C0024115
pulmonary disorder
C0034069
pulmonary fibrosis