alpha-l-iduronidase activity was assayed by incubation of a radiolabelled disaccharide , o- ( alpha-l-idopyranosyluronic acid ) - ( 1 -- -- 3 ) -2,5 anhydro-d- [ 1,3h ] -talitol 4-sulfate ( idoa-ant4s ) derived from dermatan sulfate , with homogenates of leucocytes , cultured amniotic cells and skin fibroblasts from normal individuals and patients affected with an alpha-l-iduronidase-deficiency disorder ( mucopolysaccharidosis type i , mps i ) , parents of such patients and patients affected with other mucopolysaccharidoses .
C0023786
mps i
C0026703
mucopolysaccharidoses