by using purified storage ts isolated from fibroblasts metabolically labelled with [ 3h ] glcn , no conversion of ts into ds could be demonstrated in homogenates of affected cells at either lysosomal ph ( 4.4 ) or cytosolic ph ( 6.1 ) , or in the culture medium ( ph 7.0 ) of affected cells .
C0016030
fibroblasts
C0007634
cells