similarly , o- ( beta-d-glucopyranosyluronic acid ) - ( 1 linked to 4 ) - ( 2,5-anhydro-d-mannitol-l-t 6-sulfate ) was degraded by whole-cell homogenates prepared from beta-d-glucuronidase-deficient ( mucopolysaccharidosis , type vii ) fibroblasts , to yield 2,5-anhydro-d-mannitol-l-t 5-sulfate at a rate 60-times less that that found for mps-i and normal control-preparations .
C0026703
mucopolysaccharidosis
C0023786
mps-i