the porphyrinic patients examined , and some of their relatives , showed a characteristic pattern of porphyrin production , with high uroporphyrin/coproporphyrin and ( uroporphyrin + heptacarboxylic porphyrins ) /coproporphyrin ratios , at least partly ascribable to increased uroporphyrinogen i synthetase ( ec 4.2.1.8 ) activity in patients ' hemolysates , and also to a relative deficiency of uroporphyrinogen decarboxylase .
C0032712
porphyrin
C0042093
uroporphyrin