the case is presented of a child with early manifestations of hand-schuller-christian disease limited to exophthalmos , and rapid final progression towards a clinical picture dominated by intracranial hypertension and cerebellar involvement , caused by massive histiocytic infiltration of the cerebellum , combined with discrete subdural deposits of xanthomatous tissue and minor deposits in other parts of the central nervous system and other organs .
C0019621
hand-schuller-christian disease
C0015300
exophthalmos