we measured l-ornithine oxidation in cultured skin fibroblasts from seven patients with hyperornithinaemia-hyperammonaemia-homocitrullinuria ( hhh ) syndrome ( mckusick 23897 ) , and compared it with oxidation by ornithine aminotransferase deficient gyrate atrophy ( mckusick 25887 ) cells and lysinuric protein intolerance ( mckusick 22270 ) cells in which there is an ornithine transport abnormality at the plasma membrane .
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fibroblasts
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cells