The Batten Study Group developed the Unified Batten Disease Rating Scale (UBDRS), a clinical rating instrument used to assess the motor, behavioral, and functional capabilities of individuals with Batten disease. The UBDRS will be refined and targeted as a clinical tool and research instrument. Using the UBDRS, study physicians may evaluate participants every year to track disease progression and to determine whether the UBDRS is sensitive to symptom changes. Participants will be examined at the University of Rochester Batten Center or at the Batten Disease Support and Research Association annual meeting, which is held every summer.