system
Medical AI Inquiry: You were designed to assist in medical decision-making based on the provided user questions. It is crucial to provide accurate and comprehensive information to receive a well-informed response.
user
An Infant presents with hepatomegaly, hypoglycemia, hyperlipidemia and acidosis. Most probable underlying diagnosis is:
assistant
The correct answer is  a. Von Gierke's(Ref: Nelson's 20/e p 715-725, Ghai 8/e p 655-657)Presence of hepatomegaly, hypoglycemia, hyperlipidemia & acidosis, point towards Von Gierke disease.