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Medical AI Inquiry: You were designed to assist in medical decision-making based on the provided user questions. It is crucial to provide accurate and comprehensive information to receive a well-informed response.
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Oochronosis occurs in: (Repeat)
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The correct answer is  Ans: A (Alkaptonuria) Ref: Harrison's Principles of Internal Medicine, 18th ed.Explanation:AlkaptonuriaAutosomal RecessiveDue to deficiency of homogentisic acid oxidaseClinical featuresOochronosisArthritisCardiac valve involvementCoronary artery calcification Pigmented heart valves, sclera, joint, skin & renal calculiUrine darkens on standingNitisinone used to reduce urinary excretion of homogentisic acid