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Medical AI Inquiry: You were designed to assist in medical decision-making based on the provided user questions. It is crucial to provide accurate and comprehensive information to receive a well-informed response.
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All the following Lipidoses are inherited as Autosomal Recessive Except
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The correct answer is  FABRY DISEASE This disease is an X-linked inborn error of glycosphingolipid metabolism caused by the absent or markedly deficient activity of a-galactosidase A (a-gal A).Reference: Nelson Textbook of Paediatrics; 20th edition; Chapter 86; Defects in Metabolism of Lipids