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Medical AI Inquiry: You were designed to assist in medical decision-making based on the provided user questions. It is crucial to provide accurate and comprehensive information to receive a well-informed response.
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True about nephrogenic diabetes insipidus in children –
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The correct answer is  In nephrogenic diabetes insipidus, level of the ADH is normal.
The defects lies in the distal tubule where the cells fail to respond to ADH.
Diabetes inspidus is associated with wolfram syndrome or DIDMOD syndrome not wilm's tumour.
Wolfram syndrome → Diabetes insidus, Diabetes mellitus, Optic atrophy, Deafness.