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Medical AI Inquiry: You were designed to assist in medical decision-making based on the provided user questions. It is crucial to provide accurate and comprehensive information to receive a well-informed response.
user
Metabolic abnormalities in which jaundice is seen are all of the following except?
assistant
The correct answer is  a. Von Gierke disease(Ref: Nelson 20/e p 716)In Von Gierke disease, hepatic carbohydrate metabolism is affected, which is responsible for plasma glucose homeostasis. So, fasting hypoglycemia and hepatomegaly is seen. Despite, marked hepatomegaly, the liver transaminase levels are usually normal or only slightly elevated. Jaundice is usually not seen.