###Rationale: Ocular involvement occurs in 20-35% of cases. Involvement is assynzetrical. The two pathognomic changes are -


Retinal pigmentary changes with mottled diffuse hypopigmentation.
Abnormal peripheral retinal vessels with areas of non perfusion (a vascularity).

###Answer: OPTION D IS CORRECT.
###Question: True about incontinenta pigmenti include the following except –
###Options:
A. X-linked dominant
B. Primary skin abnormality
C. Avascularity of peripheral retina
D. Ocular involvement is seen in almost 100% cases and is typically unilateral
