Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) Sandhoff Disease ?
    ### Response:
    Sandhoff disease is a rare, inherited lipid storage disorder that progressively destroys nerve cells in the brain and spinal cord. It is caused by a deficiency of the enzyme beta-hexosaminidase, which results in the harmful accumulation of certain fats (lipids) in the brain and other organs of the body.
    