Below is an instruction from Human. Write a response.
    ### Instruction:
    What causes Ovarian sex cord tumor with annular tubules ?
    ### Response:
    What causes an ovarian sex cord tumor with annular tubules? Approximately one third of ovarian sex cord tumors with annual tubules (SCTATs) develop because of an underlying genetic condition called Peutz Jeghers syndrome (PJS), which is caused by a mutation in the STK11 gene.
    