Below is an instruction from Human. Write a response.
    ### Instruction:
    How to diagnose Tietz syndrome ?
    ### Response:
    How is Tietz syndrome diagnosed? A diagnosis of Tietz syndrome is suspected in people with severe, bilateral (both ears) sensorineural hearing loss; fair skin; and light-colored hair. Identification of a change (mutation) in the MITF gene also supports this diagnosis.
    