Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) succinyl-CoA:3-ketoacid CoA transferase deficiency ?
    ### Response:
    Succinyl-CoA:3-ketoacid CoA transferase (SCOT) deficiency is an inherited disorder that impairs the body's ability to break down ketones, which are molecules produced in the liver during the breakdown of fats.  The signs and symptoms of SCOT deficiency typically appear within the first few years of life.
    