Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) 2-methylbutyryl-CoA dehydrogenase deficiency ?
    ### Response:
    2-methylbutyryl-CoA dehydrogenase deficiency is a metabolic disorder in which individuals lack adequate levels of an enzyme called 2-methylbutyryl-CoA dehydrogenase. This enzyme assists in the processing of a particular amino acid called isoleucine. The inability to process isoleucine correctly leads to the buildup of the amino acid in the body.
    