Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) SCOT deficiency ?
    ### Response:
    SCOT deficiency is a metabolic disease that is caused by reduced or missing levels of 3-ketoacid CoA transferase. This enzyme is necessary for the body to use ketones. Ketones are substances produced when fat cells break down and are an important source of energy, especially when there is a shortage of glucose.
    