Below is an instruction from Human. Write a response.
    ### Instruction:
    What are the symptoms of Tietz syndrome ?
    ### Response:
    What are the signs and symptoms of Tietz syndrome? The signs and symptoms of Tietz syndrome are usually present at birth and may include: Severe, bilateral (both ears) sensorineural hearing loss Fair skin Light-colored hair Blue eyes The Human Phenotype Ontology provides the following list of signs and symptoms for Tietz syndrome.
    