Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) Behr syndrome ?
    ### Response:
    Behr syndrome is a disorder mainly characterized by early-onset optic atrophy, ataxia, and spasticity. Other signs and symptoms may be present and vary from person to person.  Although the exact cause is unknown, the syndrome is believed to be genetic and inherited in an autosomal recessive fashion, in most cases.
    