Below is an instruction from Human. Write a response.
    ### Instruction:
    What are the genetic changes related to Bjrnstad syndrome ?
    ### Response:
    Bjrnstad syndrome is caused by mutations in the BCS1L gene. The protein produced from this gene is found in cell structures called mitochondria, which convert the energy from food into a form that cells can use. In mitochondria, the BCS1L protein plays a role in oxidative phosphorylation, which is a multistep process through which cells derive much of their energy.
    