Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) otospondylomegaepiphyseal dysplasia ?
    ### Response:
    Otospondylomegaepiphyseal dysplasia (OSMED) is a skeletal disorder characterized by skeletal abnormalities, distinctive facial features, and severe hearing loss. The condition involves the ears (oto-), affects the bones of the spine (spondylo-), and enlarges the ends (epiphyses) of long bones in the arms and legs.
    