Below is an instruction from Human. Write a response.
    ### Instruction:
    What are the genetic changes related to Friedreich ataxia ?
    ### Response:
    Mutations in the FXN gene cause Friedreich ataxia. This gene provides instructions for making a protein called frataxin. Although its role is not fully understood, frataxin appears to be important for the normal function of mitochondria, the energy-producing centers within cells.
    