Below is an instruction from Human. Write a response.
    ### Instruction:
    What is (are) Progressive deafness with stapes fixation ?
    ### Response:
    Progressive deafness with stapes fixation, also known as Thies Reis syndrome, is a form of conductive or mixed hearing loss caused by fixation of the stapes. The stapes is one of the tiny bones in the middle ear. It rests in the entrance to the inner ear, allowing sounds to pass to the inner ear.
    