Congenital anomaly of cerebrovascular system [747.81] / Hereditary hemorrhagic telangiectasia [448.0], Reason for Study: ^Reason: 3T Scanner, please evaluate for cerebral AVMs History: HHT No evidence of acute ischemic or hemorrhagic lesion on the scan.There is focal CSF filled cleft on the left posterior temporal lobe which extends from cortical surface to the left lateral ventricle. The cleft was lined with gray mater without evidence of encephalomalacia indicating focal open lip schizencephaly.Septum pellucidum, optic chiasm and bilateral optic nerves appear to be normal in size, shape and MR signal intensity. There is no evidence of cortical dysplasia.There is no mass, mass effect, edema, midline shift, intra or extra-axial fluid collection/hemorrhage, restricted diffusion/acute ischemia, or abnormal contrast enhancement. The midline structures and cranial-cervical junction are normal. The mastoid air cells are clear. Fluid collections on the right maxillary sinus.3D time of flight MOTSA MRA brain images with maximum intensity projections of the anterior/posterior intracranial circulation demonstrate normal ICAs, MCAs and ACAs. Vertebrobasilar system appears to be normal. The left distal vertebral artery is hypoplastic.There is no evidence of intracranial arterial aneurysm or arterial luminal stenosis. There is no evidence of aggregated or increased vascular signal void or focal enhancement on this scan.
1. Open lip schizencephaly on the left temporal lobe posterior aspect.2. No evidence of acute ischemic or hemorrhagic lesion on this scan.3. Normal brain MRA 