Male, 4 months old. Klippel-Trenaunay malformation left leg. There is extensive circumferential thickening and edema of the superficial soft tissues of the left lower extremity, extending from level of the hip to the ankle. Multiple lobulated fluid collections are noted, compatible with vascular malformations, particularly in the left gluteal region, with extension across the midline to the contralateral buttock and gluteal musculature as well as extension into the left pelvis. The deep veins of the left lower extremity appear hypoplastic, including inability to visualize a normal popliteal vein. Multiple dilated vascular structures are noted within the lateral soft tissues (series 1001, images 21, 29, 40; series 1101, image 4) likely corresponding to persistent embryonic veins. Patchy areas of soft tissue enhancement correlating with vascular malformations, without significant abnormal enhancement about any of the larger collections to indicate superimposed infection.The osseous structures and muscles are symmetric compared to the contralateral lower extremity.
Extensive subcutaneous soft tissue thickening/edema and multiple fluid collections, compatible with a known history of Klippel-Trenaunay syndrome and multiple vascular malformations. Hypoplastic deep veins and dilated superficial vascular structures throughout the lower extremity, likely corresponding to persistent embryonic veins.