55 year old female with primary right ventricular myopathy. Left VentricleThe left ventricle is normal in size with normal systolic function. The overall LV ejection fraction is 65%. The LVEDV is 94 ml (normal range 109+/-23), LV end diastolic volume index is 48 ml/m2 (normal range: 65+/-11), LVESV is 32 ml (normal range 31+/-10), and LV end systolic volume index is 17 ml/m2 (normal range 18+/-5). The LV mass is 79 g (normal range 114+/-24) and the LV mass index is 41 g/m2 (normal range 67+/-11). There are no regional wall motion abnormalities present. There is diastolic flattening of the interventricular septum suggesting the presence of right ventricular volume overload. There is no late gadolinium enhancement to suggest the presence of an underlying fibrosing, infiltrative, or inflammatory process.There is no LV thrombus. Left AtriumThe left atrium is normal in size. No evidence of atrial septal defect. Right VentricleThe right ventricle is severely dilated with normal systolic function. The overall RV ejection fraction is 61%, the RV end diastolic volume index is 151 ml/m2 (normal range 69+/-14), the RVEDV is 295 ml (normal range 110+/-24), the RV end systolic volume index is 59 ml/m2 (normal range 22+/-8), and the RVESV is 116 ml (normal range 35+/-13). No evidence of focal aneurysm or fatty infiltration.Right AtriumThe right atrium is severely dilated. Aortic ValveThe aortic valve is trileaflet, opens widely and there is no significant aortic regurgitation.Mitral ValveThe mitral valve opens widely and there is no significant mitral regurgitation.Pulmonic ValveThe pulmonic valve opens widely. There is no significant pulmonic regurgitation.Tricuspid ValveThe septal leaflet is apically displaced (1.6cm), relative to the mitral valve plane. There is severe malcoaptation of the leaflets. There is severe tricuspid regurgitation.AortaThere is a left sided aortic arch with a normal brachiocephalic branching pattern. The aortic root is normal in size.Pulmonary VeinsAll four pulmonary veins drain normally into the left atrium.Pulmonary ArteryThe main pulmonary artery is normal in size. Venous AnatomyThe SVC is normal in size and drains normally into the right atrium. Severe dilation of the IVC.PericardiumThere is no obvious pericardial disease.Extracardiac FindingsThis study is not designed for the specific evaluation of extra-cardiac findings; therefore, the differentiation between artifacts and real extracardiac pathology may be difficult. If clinically indicated, a separate dedicated evaluation should be considered.
1. Normal left ventricular size and systolic function (LVEF 65%) without evidence of underlying myocardial fibrosis inflammation or infiltration.2. Severe right ventricular dilation with normal systolic performance (RVEF 61%) without evidence of focal wall motion abnormality or fatty infiltration.3. Severe right atrial dilation4. Severe tricuspid regurgitation with mild coaptation of the tricuspid leaflets. The septal leaflet of the tricuspid valve is apically displaced relative to the mitral valve plane which is somewhat consistent with an Ebstein-like abnormality.5. Severe IVC dilation. 6. No evidence of atrial septal defect. No evidence of anomalous pulmonary venous return.I personally reviewed the Images and/or procedure with the Resident/Fellow and agree with this report.