Seizures, hearing problems, and developmental delay. Brain: There is no evidence of intracranial hemorrhage, mass, or acute infarct. The brain parenchymal signal appears unremarkable. There is no abnormal intracranial enhancement. The supratentorial ventricles and sulci are mildly prominent diffusely. The cerebellum is unremarkable. There is no midline shift or herniation. The major cerebral flow voids are intact. The orbits, paranasal sinuses, and scalp soft tissues are grossly unremarkable. There are small nasopharyngeal retention cysts.Internal Auditory Canals: The bilateral cochleas are small, with deficiency apical and most of the middle turns. The bilateral vestibules also appear to be mildly dysplastic and there appears to be dehiscence of the right superior semicircular canals. There are enlarged bilateral endolymphatic ducts and sacs, left larger than right. The bilateral cranial nerve 7 and 8 complexes appear to be intact. There is no evidence of mass lesions. The bilateral mastoid air cells and middle ears also appear unremarkable.
1. Findings compatible with bilateral incomplete partition type 2, left more pronounced than right.2. Mild diffuse supratentorial cerebral volume deficiency, but no evidence of gross neuronal migration anomalies.