Male, 6 years old, with GTC seizure activity, history of Dandy-Walker, developmental delay, autism, epilepsy. The left cerebellar hemisphere is hypoplastic and the fourth ventricle communicates with a large posterior fossa CSF space. The left aspect of the posterior fossa is relatively larger than the right. No torcular-lambdoid inversion is seen.Supratentorially, no significant structural abnormalities are detected. No areas of signal abnormality or edema are seen. The ventricles demonstrate normal size and morphology. No findings are seen to suggest intracranial hemorrhage. The mesial temporal lobe structures are symmetric and unremarkable.
Findings are seen in the posterior fossa which may represent a Dandy-Walker spectrum anomaly, though they do not fulfill criteria for a classic Dandy-Walker malformation. Supratentorially, the evaluation is unremarkable with no specific findings to account for the patient's seizures.