Audiogram demonstrated normal hearing in the left ear and new severe to profound loss in the right. Developmental delay, aortic coarctation, and webbed neck. Brain MRI: There is no evidence of intracranial hemorrhage, mass, or acute infarct. However, there is encephalomalacia involving the left lateral cerebellum. The supratentorial brain parenchyma and pituitary gland otherwise appear unremarkable. There is no evidence of abnormal enhancement. The ventricles and basal cisterns are normal in size and configuration. There is no midline shift or herniation. The major cerebral flow voids are intact. There is diffuse mild paranasal sinus mucosal thickening. There are bilateral staphylomas related to high myopia. The cranial appears to be microcephalic.Internal Auditory Canals: The exam is severely limited by motion artifact. There is a diffusely narrow right internal auditory canal, measuring 3 mm in diameter. There is deficiency of the right modiolus, with a scala communis and deficiency of the apical turn. In addition, the right endolymphic duct is enlarged. The left inner ear structures appear to be normal. There is scattered fluid within the bilateral middle ears and mastoid air cells. There is no evidence of mass or abnormal enhancement is within the cerebellopontine angle, cisterns bilaterally or within the internal auditory canals.
1.Narrow right internal auditory canal with apparent deficiency of the right cochlear and vestibular nerves, as well as findings suggestive of mild incomplete partition type 2.2.Bilateral tympanomastoid effusions. 3.A small area of encephalomalacia involving the lateral superior left cerebellar hemisphere may represent a prior infarct. 4.Findings suggestive of pansinusitis.5.Findings suggestive of microcephaly. The constellation of some of the imaging findings and reported clinical features is suggestive of Turner syndrome.I personally reviewed the Images and/or procedure with the Resident/Fellow and agree with this report.