This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Biochemistry
A patient presents with Von-Gierk's disease and ketosis was detected on investigation. All of the following would he associated findings except: 
Select and explain. 
A. There is hypoglycemia, B. Have low blood sugar levels, C. Oxaloacetate is required for gluconeogenesis, D. Low fat mobilization
D: Low fat mobilization
Answer: D: Low fat mobilization 
Explanation: Ans. d. Low fat mobilization (Ref Harper 's 27/e p/66)Excessive fatty acid mobilization (not the Low fat mobilization) from adipose tissues leads to ketosis in Von-Gierke's disease. Von Gierke's Disease:Type I glycogen storage disorder, inherited as autosomal recessiveQ, due to the deficiency of glucose-6 phosphataseDeficiency of glucose-6 phosphatase leads to low blood sugar and hypoglycemic attacks.Gluconeogenesis is enhanced, that's why Oxaloacetate is required for gluconeogenesis Excessive fatty acid mobilization from adipose tissues leads to ketosis