esophageal atresia is an anatomical and physiological disorder of the esophagus requiring urgent surgical intervention . the most common early complications of esophageal atresia repair include leakage of the anastomosis , recurrent tracheoesophageal fistula , and anastomotic stricture . we present a case of atypical postoperative complication in the form of pulmonary torsion comprising the middle lobe of the right lung . a 3,260  g preterm female neonate , delivered at 38 weeks ' gestation , evaluated at 7/8 points in apgar scale , was referred to our department with prenatally diagnosed esophageal atresia . on contrast , chest x - ray performed directly after birth the presence of congenital defect  esophageal atresia with tracheoesophageal fistula  was confirmed ( the upper end of esophagus visible at the level of th45 , dilated intestinal loops filled with air ) . the child was operated on the second day of life by the right laterodorsal thoracotomy . the tracheoesophageal fistula was dissected and sutured , and esophago - esophageal anastomosis was performed . before closure , the lungs were aerated by forced ventilation , continued until all collapsed regions fully expanded . during postoperative course , on control chest x - rays , there was atelectasis in the upper lobe and the middle lobe of the right lung ( fig . contrast - enhanced computed tomographic ( ct ) scan was performed and revealed abrupt termination of the bronchial airways with atypical course of horizontal interlobal fissure ( fig . right pulmonary artery was visible , its lobar branches hardly visible ; right main bronchus showed typical diameter for approximately 7  mm from the bifurcation , then narrowed to approximately 1.5  mm ( compression from outside ? ) and continued as a single bronchus to the lower lobe . thus , bronchography was performed , which showed obstruction of the upper lobe bronchus and bronchus intermedius and the middle lobe bronchus of the right lung ( fig . the patient was qualified for tracheobronchoscopy , which confirmed occlusion of the upper and middle lobar bronchi ( trachea  wide , smooth , site of sutured fistula wide , patent , tracheal bifurcation normal . main bronchus : left , normal ; right , narrowing at  10  mm from bifurcation , with a small fissure in the sagittal plane ) . the neonate was qualified for second thoracotomy on the ninth day of life . on exploration , massive infarction of the upper and middle lobe of the right lung was revealed . a 180-degree rotation of the right middle lobe in a clockwise direction was found , which caused traction and compression of vessels to the upper lobe . the lobe was untwisted , with return of inflation in the upper lobe under vision . in the middle lobe after detorsion inflation was seen only in fragments , however significant decrease of edema and hemostasis was seen , thus no resection was attempted . postoperatively , the patient recovered normal respiratory function ( initially ventilation synchronized intermittent mandatory ventilation with low parameters , from 20th postoperative day spontaneous respiration , chest drain closed on 3rd postoperative day , removal of the drain on the 5th postoperative day , feeding via gastric tube from 3rd postoperative day , discharged home on 35th postoperative day ) . the patient was then transferred to a cardiology department for diagnostics of arrhythmia and later , at the age of 5 months , to a specialist pulmonary hospital , where the middle lobe was removed because of atelectasis . torsion of a lobe of a lung is a severe , life - threatening event , though extremely uncommon . it may occur spontaneously after thoracic trauma , thoracic or cardiac surgery.1 
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 7 in children , it is considerably less frequent than in adults . so far , according to our knowledge , only nine cases have been described in pediatric literature , including one case of lung torsion complicating tracheoesophageal fistula repair.1 
 2 mortality in adult patients ranges from 12 to 16%.8 pulmonary torsion causes clinical deterioration in the face of normal arterial blood gases and requires a high index of suspicion for diagnosis . the diagnosis is usually suggested on chest x - ray and confirmed by ct scans . on chest x - rays consolidation and opacification of the affected lung fragment , bronchial cutoff or distortion with mediastinum shift and lobar air trapping can be seen.9 
 10 the diagnosis was delayed by 14 days in some reports8 
 11 because of unequivocal results of imaging studies and the fact that clinical findings may be seemingly inconspicuous . pediatric patients may present with tachycardia , fever , tachypnea , abnormal blood tests , reduced breath sounds or chest movements , dullness to percussion , and increased respiratory effort.5 
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 8 if pulmonary torsion is suspected basing on clinical history and plain radiographs , chest ct scan should be performed . ct findings comprise bronchial obstruction or distortion and abnormal pattern of blood vessels.3 
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 10 bronchoscopy is a useful tool in the diagnosis of pulmonary torsion.9 
 10 a complete interlobar fissure , with no parenchymal bridges between the neighboring lobes , and an absent inferior pulmonary ligament have been described as predisposing factors.2 the accepted treatment of pulmonary torsion is detorsion or removal of the affected lobe.10 
 11 so far , among the eight cases described in the literature , seven cases have been operated , with five resections2 
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 12 and two detorsions.1 
 6 detorsion of a lung or a lobe of doubtful viability is controversial , as it may be connected with release of inflammatory mediators and necrotic tissue , leading to a systemic response and multiorgan failure.1 
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 14 in the two described cases of detorsion , one patient recovered completely,1 whereas in the second case the lung remained shrunken and nonfunctioning.6 in this case , detorsion allowed for better assessment of the lobe viability , and decrease in edema and hemostasis were observed . in the case of our patient , the torsion was probably because of an anatomic anomaly  absence of parenchymal bridges between contiguous lobes . earlier reoperation would have probably been beneficial , but as this complication is extremely rare in the pediatric population , diagnostic process may take longer . persistent atelectasis of a lung / lobe after thoracotomy should call attention to a possibility of torsion . the following can be concluded from this case report : pulmonary torsion is a severe , life - threatening event , rarely occurring in children . early diagnosis ( x - ray / ct / bronchography / bronchoscopy ) may be lifesaving . clinical deterioration in the face of normal arterial blood gases treatment is surgical , detorsion if possible , or if the lobe is not viable  resection .