Systemic nonHodgkin lymphoma is estimated to affect 43 000 persons per year in the United States; ocular involvement is uncommon, representing approximately 2% of all extranodal lymphoma cases.(1-20) Lymphoproliferative lesions include a wide range of diseases such as benign reactive lymphoid hyperplasia, atypical lymphoid hyperplasia, and lymphoma, based on varying degrees of histopathologic and immunophenotypic features.