MalaCards based summary: Neutropenia, Severe Congenital 3, Autosomal Recessive, also known as kostmann disease, is related to severe congenital neutropenia and dentin dysplasia, type i, with microdontia and misshapen teeth, and has symptoms including neutropenia, seizures and global developmental delay.
What is a bedpan lug? Bedpan lugs are integral to closet fixtures found in many care facilities and helps with the positioning of a bedpan during cleaning. Edit
For braided ropes the standard refers to the information of the manufacturer. Klauke generally recommends the use of hexagon crimping dies according to DIN 48083, part 4 for installing of compression cable lugs DIN 46235. Range of cross section is from 6 mmÂ² up to 1000 mmÂ², bolt sizes range from 5 mm up to 20 mm.