Soil water status as a function of pressure (tension). Soil water status in natural soils can range from a flooded. condition to drainable gravitational water to plant available water. down to hydroscopic water. Tensions in natural soils do not. exceed -31,000; in this range, water is absorbed from the air.
Advanced Search. Tay-Sachs disease (the most severe form of Hexosaminidase A deficiency) is a progressive, fatal genetic condition that affects the nerve cells in the brain.
As a result, this substance accumulates to toxic levels, particularly in neurons in the brain and spinal cord. Progressive damage caused by the buildup of GM2 ganglioside leads to the destruction of these neurons, which causes the signs and symptoms of Tay-Sachs disease.