Soil water status as a function of pressure (tension). Soil water status in natural soils can range from a flooded. condition to drainable gravitational water to plant available water. down to hydroscopic water. Tensions in natural soils do not. exceed -31,000; in this range, water is absorbed from the air.
Advanced Search. Tay-Sachs disease (the most severe form of Hexosaminidase A deficiency) is a progressive, fatal genetic condition that affects the nerve cells in the brain.
Tay-Sachs disease is a rare metabolic disorder with severe neurologic (nervous system) symptoms. Metabolic refers to the body's chemical processes that produce protein and other substances, and break down nutrients to release energy.ay-Sachs disease is a metabolic disorder because it is caused by the absence of the enzyme (a type of protein) hexosaminidase A (Hex-A). Hex-A is necessary for breaking down fatty substances called lipids. Without Hex-A, these lipids build up in, and eventually destroy, the nerve cells in the brain.