The countess was accustomed to this tone as a precursor of news of something detrimental to the children's interests, such as the building of a new gallery or conservatory, the inauguration of a private theater or an orchestra.
Stiff-person syndrome (SPS) is a rare neurological disorder with features of an autoimmune disease.SPS is characterized by fluctuating muscle rigidity in the trunk and limbs and a heightened sensitivity to stimuli such as noise, touch, and emotional distress, which can set off muscle spasms.Abnormal postures, often hunched over and stiffened, are characteristic of the disorder.t is frequently associated with other autoimmune diseases such as diabetes, thyroiditis, vitiligo, and pernicious anemia. Scientists donât yet understand what causes SPS, but research indicates that it is the result of an autoimmune response gone awry in the brain and spinal cord.
A Special Purpose Entity (SPE) is a legal entity usually a limited company of some type created to fulfill narrow, specific or temporary objectives.SPE's are typically used by companies to isolate the firm from financial risk.A company will transfer assets to the SPE for management or use the SPE to finance a large project thereby achieving a narrow set of goals without putting the entire firm at risk.SPEs are also commonly used in complex financings to separate different layers of equity infusion.PE's are typically used by companies to isolate the firm from financial risk. A company will transfer assets to the SPE for management or use the SPE to finance a large project thereby achieving a narrow set of goals without putting the entire firm at risk.