A congenital<unk>  defect in which the left<unk>  is severely underdeveloped
Accounts for 2 to 3% of all congenital<unk>  disease 
With a diminutive LV, the RV must perfuse both pulmonary and systemic circulations
Survival is dependent on:
PDA (for systemic perfusion from RV to the aorta)
Nonrestrictive ASD to ensure adequate mixing of oxygenated and deoxygenated blood
PDA (for systemic perfusion from RV to the aorta)
Nonrestrictive ASD to ensure adequate mixing of oxygenated and deoxygenated blood
Hypoplastic left heart syndrome
Cyanotic
Total anomalous pulmonary venous return
Tetralogy of fallot
Transposition of the great arteries
Tricuspid atresia
Branchial cleft anomaly
Atrio-esophageal fistula