Stabilize cardiopulmonary function prior to surgery
Supplemental oxygen
Mechanical ventilation
Inotropic agents (eg, dopamine and dobutamine) improve myocardial contractility
Prostaglandin E1
Maintain adequate ductal dependent pulmonary flow
Start infusion at 0.05 mcg/kg/min IV and titrate up to 0.1 mcg/kg/min, monitoring for hypotension and apnea
Side Effects: Hypotension, Bradycardia, Seizures and Apnea
Staged surgical repair
Maintain adequate ductal dependent pulmonary flow
Start infusion at 0.05 mcg/kg/min IV and titrate up to 0.1 mcg/kg/min, monitoring for hypotension and apnea
Side Effects: Hypotension, Bradycardia, Seizures and Apnea
Tricuspid atresia
Cyanotic
Ebstein anomaly
Tetralogy of fallot
Transposition of the great arteries
Total anomalous pulmonary venous return
Atrio-esophageal fistula
Ventricular septal defect