Stabilize cardiopulmonary function prior to surgery
Maintain PDA to provide sufficient mixing of oxygenated and deoxygenated blood, and adequate systemic perfusion
Prostaglandin E1
Start infusion at 0.05 mcg/kg/min IV and titrate up to 0.1 mcg/kg/min, monitoring for hypotension and apnea
Side Effects: Hypotension, Bradycardia, Seizures and Apnea
Staged surgical repair
First stage (Norwood procedure) performed in neonates
SpO2 ranges in mid 70s-80s
Second stage (bidirectional Glenn procedure) performed at 3-6 months
SpO2 ranges in mid 70s-80s
Third stage (Fontan procedure) performed at 18-30 months
Preload dependent with SpO2 ranging from low to high 90s
Prostaglandin E1
Start infusion at 0.05 mcg/kg/min IV and titrate up to 0.1 mcg/kg/min, monitoring for hypotension and apnea
Side Effects: Hypotension, Bradycardia, Seizures and Apnea
Start infusion at 0.05 mcg/kg/min IV and titrate up to 0.1 mcg/kg/min, monitoring for hypotension and apnea
Side Effects: Hypotension, Bradycardia, Seizures and Apnea
First stage (Norwood procedure) performed in neonates
SpO2 ranges in mid 70s-80s
Second stage (bidirectional Glenn procedure) performed at 3-6 months
SpO2 ranges in mid 70s-80s
Third stage (Fontan procedure) performed at 18-30 months
Preload dependent with SpO2 ranging from low to high 90s
SpO2 ranges in mid 70s-80s
SpO2 ranges in mid 70s-80s
Preload dependent with SpO2 ranging from low to high 90s
Hypoplastic left heart syndrome
Cyanotic
Total anomalous pulmonary venous return
Tetralogy of fallot
Transposition of the great arteries
Tricuspid atresia
Branchial cleft anomaly
Atrio-esophageal fistula