Sinistrum variant most associated with other congenital cardiovascular defects in symptomatic infants
Can be incidental finding in adults as either isolated finding or in association with PFO, ASD, persistent left superior vena cava
Symptoms depend on size of opening in accessory membrane between the atria
Symptoms include dyspnea on exertion, orthopnea, easy fatiguability, low exercise tolerance, palpitations
Increased risk of thrombus formation in LA
Murmur
Elevated JVD
Hepatomegaly
Ascites
Peripheral edema
Cor triatriatum
Pericarditis
Stone heart
Pulmonary Hypertension
Hypertrophic cardiomyopathy
Right heart failure
Atrio-esophageal fistula
Atrial Myxoma