Sweat chloride test to make diagnosis, may also be diagnosed by amniocentesis if high suspicion antenatally (outside ED scope)
CBC (signs of infection)
Electrolytes
LFTs and lipase (if concern for pancreatitis)
Consider blood and sputum cultures (may have resistant organisms)
CXR
Advanced disease: peribronchial thickening, mucous plugs,<unk> /bullous lesions, atelectasis, hilar adenopathy, air trapping
Infiltrates if pneumonia
Pneumothorax
Advanced disease: peribronchial thickening, mucous plugs,<unk> /bullous lesions, atelectasis, hilar adenopathy, air trapping
Infiltrates if pneumonia
Pneumothorax
Cystic fibrosis
Cerebral palsy
Bronchopulmonary dysplasia
Brash syndrome
Tracheomalacia
Scleroderma
Down syndrome
Idiopathic pulmonary fibrosis