In an individual with dHMN<unk> , electromyography will show pure motor<unk> , patterns of weakness without upper motor neuron damage, in the hands. Tendon reflexes will also appear normal. Clinical, electrophysiological, and pathological testing will show a lack of damage to sensory neurons, differentiating this disease from CMT.
Distal hereditary motor neuropathy type V
Hereditary sensory and autonomic neuropathy type I
Familial amyloid neuropathy
Giant axonal neuropathy
Familial amyloid polyneuropathy
Distal spinal muscular atrophy type 1
Madras motor neuron disease
Distal spinal muscular atrophy type 2