<unk>  affects Indo-European populations. It is rare in East Asians, sub-Saharan Africans, and Native Americans.<unk>  is the most prevalent inherited ataxia, affecting approximately 1 in 40,000 with European descent. Males and females are affected equally. The estimated carrier prevalence is 1:100. A 1990–1996 study of Europeans calculated the incidence rate was 2.8:100,000. The prevalence rate of<unk>  in Japan is 1:1,000,000.<unk>  follows the same pattern as haplogroup R1b. Haplogroup R1b is the most frequently occurring paternal lineage in Western Europe.<unk>  and Haplogroup R1b are more common in northern Spain, Ireland, and France, rare in Russia and Scandinavia, and follow a gradient through central and eastern Europe. A population carrying the disease went through a population bottleneck in the Franco-Cantabrian region during the last ice age.
Friedreich's ataxia
Spinocerebellar ataxia type 6
Stratton Parker syndrome
Autosomal recessive cerebellar ataxia type 1
Spinocerebellar ataxia type-13
Sandhoff disease
Jokela type spinal muscular atrophy
Parkes Weber syndrome