PAMT was first described by Takahashi et al. in 2007. Estimated frequency of PAMT is less than 1/150 compared to that of gastrointestinal stromal tumors (GISTs). The prevalence is similar in both genders and can develop at any age (7–75 years). The size of tumor ranges from 1.9 to 15.0 cm and the mean value is 6.3 cm. PAMT is considered as a benign tumor, due to its histological features such as the presence of bland tumor cells, low proliferation index, low mitotic-rate, absence of necrosis and vascular invasion and no recurrence. In one case there has been reported vascular invasion, thus possibility of malignant transformation cannot be excluded. But the limited number of reported cases is insufficient to draw any conclusion. The true biological potential of PAMT remains unknown due to its infrequency.
Plexiform angiomyxoid myofibroblastic tumor
Inflammatory myofibroblastic tumour
Perivascular epithelioid cell tumour
Sclerosing epithelioid fibrosarcoma
Multinucleate cell angiohistiocytoma
Desmoplastic small-round-cell tumor
Malignant ectomesenchymoma
Angiomatoid fibrous histiocytoma