<unk>  or Pégot-Cruveilhier–Baumgarten disease is a rare medical condition in which the umbilical or paraumbilical veins are distended, with an abdominal wall bruit (the<unk><unk>  bruit) and palpable thrill, portal hypertension with splenomegaly, hypersplenism and oesophageal varices, with a normal or small liver. The presence of the<unk><unk>  venous hum is highly suggestive of portal hypertension, and is never a normal physical examination finding. It was first described by Pégot in 1833, and then by Jean<unk>  (1835) and Paul Clemens von<unk>  (1907). Armstrong et al. (1942) and Steinburg and Galambos (1967) described two different types of the condition: *<unk><unk>  syndrome: liver cirrhosis or portal hypertension is the cause of the distension of the paraumbilical veins (i.e. an acquired condition in which the veins reopen due to high portal pressure). *<unk> : the distension of the paraumbilical veins is due to failure of umbilical vein closure, with little or no evidence of liver disease found on liver biopsy (i.e. a congenital patency of the umbilical vein leading to portal hypertension).
Cruveilhier–Baumgarten disease
Tornwaldt's disease
Degos disease
Brill–Zinsser disease
Darier's disease
Fox–Fordyce disease
Chandler's disease
Helsmoortel-Van der Aa syndrome