The syndrome is defined as the following changes: * optic atrophy in the ipsilateral eye * disc edema in the contralateral eye * central scotoma (loss of vision in the middle of the visual fields) in the ipsilateral eye * anosmia (loss of smell) ipsilaterally This syndrome is due to optic nerve compression, olfactory nerve compression, and increased intracranial pressure (ICP) secondary to a mass (such as meningioma or plasmacytoma, usually an olfactory groove meningioma). There are other symptoms present in some cases such as nausea and vomiting, memory loss and emotional lability (i.e., frontal lobe signs).
Foster Kennedy syndrome
Krabbe disease
Muenke syndrome
Kaufman oculocerebrofacial syndrome
Hurler–Scheie syndrome
Warburg Micro syndrome
Poland syndrome
Cantú syndrome