Familial clustering of the disease, with several relatives being diagnosed may occur. Relatives of patients have an increased risk of developing the disease. Genetics The tumors often harbour loss of chromosome 18q. Mutations in CDKN1B are present in approximately 8% of cases.
Small intestine neuroendocrine tumor
Pancreatic neuroendocrine tumor
Goblet cell carcinoid
Neuroendocrine tumor
VIPoma
Hereditary diffuse gastric cancer
Acinar cell carcinoma of the pancreas
Metastatic insulinoma