Patients with<unk>  may present clinically with progressive or fluctuating, one sided sensorineural hearing loss which may mimick Meniere's disease due to the development of tumor associated<unk>  hydrops. Patients may also experience tinnitus, vertigo, and loss of vestibular function (ataxia). Alternatively, symptom onset may be sudden, due to intralabyrinthine hemorrhage. Patients may also present with other symptoms related to von Hippel-Lindau syndrome in other anatomic sites, which will result in imaging evaluation of the head.
Endolymphatic sac tumor
Nabothian cyst
Gonadoblastoma
Endodermal sinus tumor
Teratoma
Embryoma
Theca lutein cyst
Luteoma