Untreated,<unk>  rapidly results in progressive right ventricular hypertrophy due to the increased resistance caused by narrowing of the pulmonary trunk. This progresses to heart failure which begins in the right ventricle and often leads to left heart failure and dilated cardiomyopathy. Mortality rate depends on the severity of the<unk> . If left untreated,<unk>  carries a 35% mortality rate in the first year of life, and a 50% mortality rate in the first three years of life. Patients with untreated<unk>  rarely progress to adulthood. Patients who have undergone total surgical repair of<unk>  have improved hemodynamics and often have good to excellent cardiac function after the operation with some to no exercise intolerance (New York Heart Association Class I-II). Long-term outcome is usually excellent for most patients, however residual post-surgical defects such as pulmonary regurgitation, pulmonary artery stenosis, residual VSD, right ventricular dysfunction, right ventricular outflow tract obstruction may affect life expectancy and increase the need for reoperation. Cardiovascular and cerebrovascular complications in patients with repaired CHD such as<unk>  occur earlier in life compared to healthy subjects. Chronic pulmonary regurgitation and right ventricular dilation and dysfunction is also common. Within 30 years after correction, 50% of patients will require reoperation. The most common cause of reoperation is a leaky pulmonary valve (pulmonary valve insufficiency). This is usually corrected with a procedure called pulmonary valve replacement. One common prognostic factor with<unk>  is the development of ischemia reperfusion injury. Insufficient myocardial protection is considered one of the main causes of death in the correction of<unk> .
Tetralogy of Fallot
Cœur en sabot
Trilogy of Fallot
Double aortic arch
Transposition of the great vessels
Levo-Transposition of the great arteries
Dextro-Transposition of the great arteries
Persistent truncus arteriosus