People with<unk> tinosis lack a functioning transporter <unk> tinosin) which transports<unk> tine from the lysosome to the cytosol. This ultimately leads to buildup of<unk> tine in lysosomes, where it crystallizes and damages cells.<unk>  enters lysosomes and converts<unk> tine into<unk> teine and<unk> teine-cysteamine mixed disulfide, both of which can exit the lysosome. Biological function<unk>  also promotes the transport of L-cysteine into cells, that can be further used to synthesize glutathione, which is one of the most potent intracellular antioxidants.<unk>  is used as a drug for the treatment of<unk> tinosis; it removes<unk> tine that builds up in cells of people with the disease.
Cysteamine
Carnitine
Nicotinamide
Inositol
Homocysteine
Choline
3-Methylhistidine
Fructosamine