<unk> , sometimes known as<unk>  syndrome or progressive non-infectious anterior vertebral fusion (PAVF), is a unique spinal disorder with distinctive radiological features. This is a rare childhood<unk>  of unknown cause, affecting females slightly more than males (60%). Prevalence is unknown, but there has been reported approximately 80-100 individuals with<unk>  since 1949. However, there is still little known research due to the rarity of the<unk> . The<unk>  is so rare that the National Organization for Rare<unk> s does not even mention<unk>  in their database.<unk>  affects the lower back, as can be seen on MRI scans. It is characterized by the progressive fusion of the anterior vertebral body in the thoracolumbar region of the spine. This article discusses the background, clinical presentation, diagnosis, treatment and management, and prognosis of<unk> . Sections on clinical studies, case studies, and naming of<unk> .
Copenhagen disease
TRIANGLE disease
CHAI disease
Upington disease
BENTA disease
Caplan's syndrome
Senior–Løken syndrome
Erdheim–Chester disease