Although this disease has been known for around 70 years, the pathomechanism underlying it is still unknown. Several hypotheses have been developed regarding the underlying mechanism for<unk> . One theory suggests that inflammation of blood vessels may trigger the condition. Another theory has to do with<unk>  as a coagulopathy. Development of a thrombus and resulting reduction of blood flow is common in this condition. A reduction in blood flow throughout the body can lead to damaged endothelial cells and may perhaps lead to the formation of the characteristic papules. Another hypothesis suggests that abnormal swelling and proliferation of the vascular endothelium can lead to intestinal and central nervous system thrombosis, and ultimately lead to development of symptoms associated with<unk> . Overall, individuals with<unk>  have abnormal blockages in their arteries and veins; however, the cause of these blockages is unknown.
Degos disease
Kyrle disease
Fox–Fordyce disease
Van Buchem disease
Bayoud disease
Ollier disease
Sézary disease
Wobbler disease