Histologically, the Descemet's membrane in<unk>  becomes diffusely thickened and laminated. Multiple layers of basement membrane-like material appear to form on the posterior part of Descemet's membrane. The<unk>  cells are sparse - they become atrophic and degenerated, with many vacuoles. The corneal stroma becomes severely disorganised; the lamellar arrangement of the fibrils becomes disrupted.
Congenital hereditary endothelial dystrophy
Livedoid vasculitis
Infantile systemic hyalinosis
Lupus vasculitis
Systemic vasculitides
Hereditary hemorrhagic telangiectasia
Familial aortic dissection
Arterial tortuosity syndrome