The overall incidence was previously estimated at 0.5 to 1 cases per 100,000 people per year. Recent research in Europe indicates that the previous estimate of 1-2 persons per million may be underestimating the actual rate by approximately half, with the real incidence being approximately 3.2 persons per million, and the prevalence being 22 persons per million. It is slightly more common in women than men (male:female ratio of approximately 1:1.3,), although the actual ratio is difficult to identify due to potential misdiagnoses and possibly inclusion bias in reported studies. The median age at presentation is typically about 50 years with a range of 20–25 years, but<unk>  may strike persons of any age.
Pseudomyxoma peritonei
Primary peritoneal carcinoma
Pancreatic serous cystadenoma
Peritoneal mesothelioma
Pancreatic mucinous cystadenoma
Hepatoid tumor
Pancreatic mucinous cystic neoplasm
Pellegrini–Stieda syndrome