<unk>  is a malignant midline primitive neuroectodermal tumor occurring in patients with inherited uni- or bilateral<unk> . In most cases<unk>  presents itself as pineoblastoma (pineal<unk> . In about a fourth of the cases the tumor develops in another intracranial region, most commonly supra- or parasellar (non-pineal<unk> , but there are reported cases with non-pineal<unk>  in the 3rd ventricle. In most cases pineal<unk>  is diagnosed before the age of 5, but after the diagnosis of<unk> . Non-pineal<unk> , however, is often diagnosed simultaneous with<unk> . Prognosis of patients with<unk>  is dismal, only a few patients have survived more than 5 years after diagnosis; all survivors were diagnosed with small tumors in a subclinical stage. Recent advances in (high-dose) chemotherapy treatment regimens and early detection have improved survival of patients with<unk> .
Trilateral retinoblastoma
Ischiopatellar dysplasia
Intraocular schwannoma
Optic nerve hypoplasia
Optic nerve glioma
Nasolabial cyst
Unilateral nevoid telangiectasia
Optic nerve sheath meningioma