Standard of care for treatment of CPT<unk><unk>  commonly involves limitations on prolonged strenuous activity and the following stipulations: * The medium-chain fatty acid triheptanoin appears to be an effective therapy for adult-onset CPT<unk><unk> . * Restriction of lipid intake, increased carbohydrate intake * Avoidance of fasting situations * Glucose infusions during infections to prevent catabolism * Avoidance of valproic acid, ibuprofen, diazepam, and general anesthesia * Dietary modifications including replacement of long-chain with medium-chain triglycerides supplemented with L-carnitine * Rigorous meal schedule * Avoidance of rigorous exercise.
Carnitine palmitoyltransferase II deficiency
Carnitine palmitoyltransferase I deficiency
Carnitine-acylcarnitine translocase deficiency
3-Methylcrotonyl-CoA carboxylase deficiency
Acyl-CoA oxidase deficiency
Malonyl-CoA decarboxylase deficiency
2-Methylbutyryl-CoA dehydrogenase deficiency
Pyruvate kinase deficiency