<unk>  (KLICK syndrome) is a rare cutaneous condition characterized by ichthyosis and<unk> . It is an autosomal recessive disorder associated with a deletion in the transcription gene POMP, which codes proteasome maturation protein. This prevents the correct formation of filaggrin from profilaggrin. Sympotmatic treatment with keratolytics and retinoids is successful, but if treatment is stopped, symptoms recur.
Keratosis linearis with ichthyosis congenita and sclerosing keratoderma syndrome
Photoleukomelanodermatitis of Kobori
Pigmented hairy epidermal nevus syndrome
Harlequin-type ichthyosis
Johnson–McMillin syndrome
Vulvar childhood pemphigoid
Congenital ichthyosiform erythroderma
Beare–Stevenson cutis gyrata syndrome