In mostly European experience with 69 patients during 1996–2016, the 5- and 10-year survival rates for SCLS patients were 78% and 69%, respectively, but the survivors received significantly more frequent preventive treatment with IVIG than did non-survivors. Five- and 10-year survival rates in patients treated with IVIG were 91% and 77%, respectively, compared to 47% and 37% in patients not treated with IVIG. Moreover, better identification and management of this condition appears to be resulting in lower mortality and improving survival and quality-of-life results as of late.
Capillary leak syndrome
Sepsis
Pulmonary-renal syndrome
Polycythemia vera
Edwards syndrome
Polycythemia
Thoracic insufficiency syndrome
Hyperviscosity syndrome