<unk>  is typified by progressive and permanent cerebellar dysfunction. These cerebellar signs include ataxia and dysarthria, likely caused by cerebellar atrophy. Prior to diagnosis and the onset of major symptoms, patients often report a feeling of "wooziness" and momentary imbalance when turning corners or making rapid movements. The age at which symptoms first occur varies widely, from age 19 to 71, but is typically between 43 and 52. Other major signs of<unk>  are the loss of vibratory and proprioceptive sensation and nystagmus. While most patients present with these severe progressive symptoms, others, sometimes within the same family, display episodic non-progressive symptoms more similar to episodic ataxia. Still others present with symptoms common to both<unk>  and familial hemiplegic migraine.
Spinocerebellar ataxia type 6
Spinocerebellar ataxia type 1
Spinocerebellar ataxia type-13
Autosomal recessive cerebellar ataxia type 1
Metachromatic leukodystrophy
Stratton Parker syndrome
Friedreich's ataxia
Autosomal recessive spastic ataxia of Charlevoix-Saguenay