While UHS is thought to be extremely rare, its precise frequency and prevalence is unknown. As of 2016, there were ~100 case studies of UHS in the scientific literature and as of 2020, there are a few more documented case studies. UHS has been found in patients who also have diseases such as ectodermal dysplasia and loose anagen<unk><unk> . While sometimes observed with other disorders, it is believed that<unk>  is an isolated disease.
Uncombable hair syndrome
X-linked hypertrichosis
Dual-role transvestism
Prepubertal hypertrichosis
Adiposogenital dystrophy
Paraphrenia
Latrodectism
Panner disease