<unk>  is a rare congenital heart disorder accounting for only 0.1-0.3% of congenital heart<unk> s worldwide. It is characterized by a communication between the aortic and pulmonary arteries, with preservation of two normal semilunar valves. It is the result of an incomplete separation of the aorticopulmonary trunk that normally occurs in early fetal development with formation of the spiral septum.<unk> s occur in isolation in about half of cases, the remainder are associated with more complex heart abnormalities.
Aortopulmonary septal defect
Double aortic arch
Pulmonary artery sling
Heart septal defect
Pulmonary atresia
Double outlet right ventricle
Interrupted aortic arch
Persistent truncus arteriosus