In a nationwide study of<unk>  the median survival was 7.2 years (primary<unk> : 10.9 years; secondary<unk> : 1.7 years). Secondary<unk>  was associated with higher mortality rate than primary<unk> , with a 5-year survival of 38%. Among patients with<unk> , the prevailing causes of death were bleeding, infections, and hematological cancer. It has been observed that there is a risk of developing other autoimmune problems and hypogammaglobulinemia, in one cohort 58% of children with<unk>  had CD4-/CD8- T cells which is a strong predictor for having autoimmune lymphoproliferative<unk> .
Evans syndrome
Zaki syndrome
Walker–Warburg syndrome
Morvan's syndrome
Rabbit syndrome
Michels Caskey syndrome
Antley–Bixler syndrome
Branchio-oto-renal syndrome