Individuals with<unk>  have polyclonal B cell lymphocytosis (i.e. excess B cells) developing in infancy, in addition to splenomegaly and lymphadenopathy. Patients may have low serum IgM and mildly anergic T cells. These features likely contribute to the mild immunodeficiency seen with<unk> . Patients are generally susceptible to recurrent sinopulmonary and ear infections in childhood, and may be more susceptible to certain viruses including Epstein-Barr virus, BK virus, and molluscum contagiosum.
BENTA disease
Degos disease
Pogosta disease
TRIANGLE disease
Bahima disease
Fox–Fordyce disease
Cruveilhier–Baumgarten disease
Borna disease