The primary tumor appears to arise from the MUC2 expressing goblet cells and most commonly from these cells in the appendix. The K-Ras and p53 genes may be involved in the oncogenesis. It may be diagnosed with a range of conditions. While the majority of these cases are associated with appendiceal carcinomas, other conditions may also be found, including disseminated<unk> l adenomucinosis (DPAM),<unk> l carcinomas, several mucinous tumors (mucinous adenocarcinoma, mucinous cystadenoma, and mucinous cystadenocarcinoma), as well as other disease states. Other primary sites that have been reported include colon, rectum, stomach, gallbladder, bile ducts, small intestine, urinary bladder, lung, breast, fallopian tubes, and the pancreas.
Pseudomyxoma peritonei
Primary peritoneal carcinoma
Pancreatic serous cystadenoma
Peritoneal mesothelioma
Pancreatic mucinous cystadenoma
Hepatoid tumor
Pancreatic mucinous cystic neoplasm
Pellegrini–Stieda syndrome