<unk>  <unk>  is an increasingly recognized type of chronic pancreatitis that can be difficult to distinguish from pancreatic carcinoma but which responds to treatment with corticosteroids, particularly prednisone. Although<unk>  is quite rare, it constitutes an important clinical problem for both patients and their clinicians: the disease commonly presents itself as a tumorous mass which is diagnostically indistinguishable from pancreatic cancer, a disease that is much more common in addition to being very dangerous. Hence, some patients undergo pancreatic surgery, which is associated to substantial mortality and morbidity, out of the fear by patients and clinicians to undertreat a malignancy. However, surgery is not a good treatment for this condition as<unk>  responds well to immunosuppressive treatment. There are two categories of<unk> : Type 1 and Type 2, each with distinct clinical profiles. Type 1<unk>  is now regarded as a manifestation of IgG4-related disease, and those affected have tended to be older and to have a high relapse rate. Type 1 is associated with pancreatitis, Sjogren syndrome, Primary sclerosing cholangitis and Inflammatory bowel disease. Patients with Type 2<unk>  do not experience relapse, tend to be younger and not associated with systemic disease.<unk>  occurring in association with an<unk>  disorder has been referred to as "secondary" or "syndromic"<unk> .<unk>  does not affect long-term survival.
Autoimmune pancreatitis
Pancreatic cancer
Hereditary pancreatitis
Fibrocalculous pancreatopathy
Chronic pancreatitis
Biliary pseudolithiasis
Biliary fistula
Sialolithiasis