Families are defined as having<unk> , if the phenotype is consistent with highly penetrant autosomal dominant inheritance. In simple terms, this would require two or more first degree relatives (or three or more second degree relatives) to have unexplained recurrent-acute or chronic pancreatitis in two or more generations. It is an autosomal dominant disease with penetrance that is generally accepted to be ≈80%.
Hereditary pancreatitis
Autoimmune pancreatitis
Chronic pancreatitis
Fibrocalculous pancreatopathy
Primary sclerosing cholangitis
Whipple's disease
Primary biliary cholangitis
Secondary sclerosing cholangitis