<unk>  is characterized by many symptoms resulting from brain damage: *Sensorineural hearing loss- This is the most common symptom associated with<unk>  and its absence is rare. The highest pitches are often lost first, and over a period of one to twelve years hearing loss progresses to total deafness or loss of all hearing but low pitches. *Ataxia- The impairment of gait, which is the second most common symptom. *Pyramidal signs- Various signs that indicate a condition of the pyramidal tracts. *Dementia- Occurs in approximately one-quarter of those affected by<unk> . *Disturbances of the bladder *Anosmia- Loss of sense of smell. *Anisocoria- Unequal size of pupils.
Superficial siderosis
Geographic atrophy
Neurofibrillary tangle
Polymicrogyria
Posterior cortical atrophy
Amyloid plaques
Hippocampal sclerosis
Hemosiderin hyperpigmentation