No treatment is indicated for<unk> , while the degree of<unk>  depends on the dietary fructose intake, it does not have any clinical manifestations. The amount of fructose routinely lost in urine is quite small. Other errors in fructose metabolism have greater clinical significance. Hereditary fructose intolerance, or the presence of fructose in the blood (fructosemia), is caused by a deficiency of aldolase B, the second enzyme involved in the metabolism of fructose. This enzyme deficiency results in an accumulation of fructose-1-phosphate, which inhibits the production of glucose and results in diminished regeneration of adenosine triphosphate. Clinically, patients with hereditary fructose intolerance are much more severely affected than those with<unk> , with elevated uric acid, growth abnormalities and can result in coma if untreated.
Essential fructosuria
Aspartylglucosaminuria
Hawkinsinuria
Alkaptonuria
Orotic aciduria
Urocanic aciduria
Glycosuria
Dicarboxylic aminoaciduria