<unk>  is usually caused by a hemangioendothelioma or other vascular tumor, often present at birth. Although these tumors are relatively common, they only rarely cause<unk> . When these tumors are large or are growing rapidly, sometimes they can trap platelets, causing severe thrombocytopenia. The combination of vascular tumor and consumptive thrombocytopenia defines<unk> . Tumors can be found in the trunk, upper and lower extremities, retroperitoneum, and in the cervical and facial areas. This consumptive coagulopathy also uses up clotting factors, such as fibrinogen which may worsen bleeding. The coagulopathy can progress to disseminated intravascular coagulation and even death. Hemolytic anemia secondary to microangiopathic destruction (physical damage) of the RBCs can be expressed as mild, moderate, or severe.
Kasabach–Merritt syndrome
Rapp–Hodgkin syndrome
Bare lymphocyte syndrome type II
Pitt–Hopkins syndrome
Schwartz–Jampel syndrome
Hypotrichosis–lymphedema–telangiectasia syndrome
Schwartz–Matsuo syndrome
Bare lymphocyte syndrome