The<unk>  is in<unk> . The skin lesions occur on cheeks, nose, fingers, toes and soles. They may vary in appearance but frequently develop into non-healing ulcers. Interstitial lung disease is also common. Some individuals may not experience any obvious skin issues. All affected children fail to thrive. Other features include myositis and joint stiffness. Some children experience hyper mobility, and joint pain. Imaging: Chest X rays show sign consistent with interstitial lung disease. Bloods: Anemia, leukopenia, thrombocytosis, T cell lymphopenia with normal B cells and hypergammaglobulinemia may occur. Autoantibodies may be present including antinuclear, antiphospholipid, and anticardiolipin antibodies. The erythrocyte sedimentation rate and C reactive protein levels tend to be raised. Biopsies: Skin biopsies show inflammation of the capillaries and microthrombosis. Immunoglobulin M and C3 deposition may be present. Lung biopsies show alveolitis, follicular hyperplasia, B-cell germinal centers and interstitial fibrosis. Some children demonstrate pulmonary alveolar protianosis on Lavage.
STING-associated vasculopathy with onset in infancy
Livedoid vasculitis
Congenital hereditary endothelial dystrophy
Lupus vasculitis
Golfer's vasculitis
Systemic vasculitides
Roussy–Lévy syndrome
Retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestations