Treatment is based on: * PGE1 to maintain patent ductus arteriosus * modified Blalock-Taussig shunt to maintain pulmonary blood flow by placing a Gore-Tex conduit between the subclavian artery and the pulmonary artery. * where too much flow to the lungs is present, a pulmonary band may be placed in a first operation * cavopulmonary anastomosis (hemi-Fontan or bidirectional Glenn) to provide stable pulmonary flow * Fontan procedure to redirect inferior vena cava and hepatic vein flow into the pulmonary circulation
Tricuspid atresia
Double aortic arch
Interrupted aortic arch
Persistent truncus arteriosus
Double outlet right ventricle
Double inlet left ventricle
Situs ambiguus
Transposition of the great vessels