Surgery is curative despite possible local relapses. Wide resection of the tumor and resection arthrodesis with an intramedullary nail, vertebrectomy and femoral head allograft replacement of the vertebral body, resection of the iliac wing and hip joint disarticulation have been among the performed procedures. The close resemblance of FCMB to<unk>  dysplasia has suggested to some scholars that they might be closely related entities, although the latter features woven bone trabeculae without osteoblastic rimming, which is a quite distinctive aspect. Instead, the occurrence of epiphyseal plate-like cartilage is peculiar of the former.
Fibrocartilaginous mesenchymoma of bone
Juvenile active ossifying fibroma
Peripheral ossifying fibroma
Osteoblastoma
Solitary fibrous tumor
Malignant ectomesenchymoma
Giant-cell tumor of bone
Aneurysmal bone cyst