<unk>  also known as<unk><unk> glycinuria or BMCC deficiency is an inherited disorder in which the body is unable to process certain proteins properly. People with this disorder have inadequate levels of an enzyme that helps break down proteins containing the amino acid leucine. This condition affects an estimated 1 in 50,000 individuals worldwide.
3-Methylcrotonyl-CoA carboxylase deficiency
2-Methylbutyryl-CoA dehydrogenase deficiency
Glutaminase deficiency
Pyruvate kinase deficiency
Malonyl-CoA decarboxylase deficiency
2,4 Dienoyl-CoA reductase deficiency
3-Hydroxy-3-methylglutaryl-CoA lyase deficiency
Multiple carboxylase deficiency