The disease is an inherited autosomal dominant disease, but the physiological cause of the<unk>  is still unclear. An acidophyllic mucopolysaccharide-containing substance was discovered, especially in cochleas, maculas, and crista ampullaris of patients with DFNA9 (a chromosome locus), as well as severe degeneration of vestibular and cochlear sensory axons and dendrites. It is suggested that the mucopolysaccharide deposit could cause strangulation of nerve endings. The maculas and crista ampullaris are what allow for non-visual sensation of head movements. The crista ampullaris resides in the semicircular canals of the inner ear and detects angular acceleration, while the maculas are housed within the vestibule of the inner ear and detect linear acceleration. When affected, these organs can lead to vertigo and nausea because the body would always feel off-balance.
Vestibulocochlear dysfunction progressive familial
Causes of hearing loss
medical cause of Tinnitus
symptom of Benign paroxysmal positional vertigo
symptom of Scintillating scotoma
medical diagnosis of Septo-optic dysplasia
Social impact of profound hearing loss
Chronic cerebrospinal venous insufficiency controversy