Onset of symptoms usually occur in early adulthood and is characterized by intention tremor, progressive ataxia, convulsions, and myoclonic epileptic jerks. Tremors usually affect one extremity, primarily the upper limb, and eventually involve the entire voluntary motor system. Overall, the lower extremity is usually disturbed less often than the upper extremity. Additional features of the syndrome include: an unsteady gait, seizures, muscular hypotonia, reduced muscular coordination, asthenia, adiadochokinesia and errors with estimating range, direction, and force of voluntary movements. Mental deterioration can, rarely, occur.
Ramsay Hunt syndrome type 1
Ramsay Hunt syndrome type 2
Tolosa–Hunt syndrome
Robinow syndrome
Dandy–Walker malformation
Autosomal dominant porencephaly type I
Seaver Cassidy syndrome
Lateral meningocele syndrome