Even though there is often a very dramatic and rapidly enlarging, destructive tumor, there is usually a benign clinical course after complete local excision (usually by partial maxillectomy) with clear or free surgical margins. In rare cases, chemotherapy may be used for recurrent or residual tumors. Overall, the outcome is good, although it is quite unpredictable, with about 30% of patients have a recurrence. In about 10% of cases, metastasis may be seen (lymph nodes, liver, bone and soft tissue).
Melanotic neuroectodermal tumor of infancy
Infantile hemangiopericytoma
Primitive neuroectodermal tumor
Neuroma cutis
Pediatric ependymoma
Retinoblastoma
Neurothekeoma
Ameloblastoma