The majority of patients with<unk>  are asymptomatic and therefore have a good prognosis with few complications. Most are not diagnosed, so definitive data in not available. For symptomatic patients, the prognosis is far worse. In patients without the presence of melanoma, more than 50% die within 3 years of displaying symptoms. While those with malignancy have a mortality rate of 77% with most patients displaying symptoms before the age of 2. The presence of a Dandy-Walker malformation along with<unk> , as occurs in 10% of symptomatic patients, further deteriorates prognosis. The median survival time for these patients is 6.5 months after becoming symptomatic.
Neurocutaneous melanosis
Nevus anemicus
Phakomatosis pigmentokeratotica
Granulomatous slack skin
Blue nevus
Erythema dyschromicum perstans
Sparganosis
Hypertrichosis cubiti