Tissue biopsy is the diagnostic modality of choice. Due to a high incidence of lymph node involvement, a sentinel lymph node biopsy is often performed. A common characteristic of<unk>  (observed in 80% of all cases) is the loss of function of the SMARCB1 gene (also termed BAF47, INI1, or hSNF5). Immunohistochemical staining of INI1 is available and can be used for the diagnosis of<unk> . MRI is the diagnostic modality of choice for imaging prior to biopsy and pathologic diagnosis, with the primary role being the determination of anatomic boundaries. Staging The staging for<unk>  takes into account size and location of the primary tumor, lymph node involvement, presence and location of metastasis, and histologic grade (a measure of disease aggressiveness)
Epithelioid sarcoma
Angiomatoid fibrous histiocytoma
Alveolar soft part sarcoma
Sclerosing epithelioid fibrosarcoma
Undifferentiated pleomorphic sarcoma
Mast cell sarcoma
Hemangiosarcoma
Adenomatoid tumor