<unk>  is a genetic disorder in which a person has a defective gene for lipoprotein<unk> , which leads to very high triglycerides, which in turn causes stomach pain and deposits of fat under the skin, and which can lead to problems with the pancreas and liver, which in turn can lead to diabetes. The disorder only occurs if a child acquires the defective gene from both parents (it is autosomal recessive). It is managed by restricting fat in diet to less than 20 g/day.
Lipoprotein lipase deficiency
Lecithin cholesterol acyltransferase deficiency
Apolipoprotein B deficiency
Lysosomal acid lipase deficiency
Acyl-CoA oxidase deficiency
Glycerol kinase deficiency
Acid lipase disease
2,4 Dienoyl-CoA reductase deficiency