<unk>  <unk>  is a very rare malignant tumor of soft tissues that on microscopic examination consists of small round or ovoid neoplastic<unk>  fibroblast-like cells, i.e. cells that have features resembling both<unk>  cells and fibroblasts. In 2020, the World Health Organization classified<unk>  as a distinct tumor type in the category of malignant fibroblastic and myofibroblastic tumors. However, current studies have reported that low-grade fibromyxoid sarcoma (LGFMS) has many clinically and pathologically important features characteristic of<unk> ; these studies suggest that LGSFMS may be an early form of, and over time progress to become, a<unk> . Since the World Health Organization has classified LGFMS as one of the malignant fibroblastic and myofibroblastic tumors that is distinctly different than<unk> ,<unk>  and LGFMS are here regarded as different tumor forms.<unk> s are aggressive tumors that usually develop in adults and elderly individuals or, in a small minority of cases, children.<unk>  tumors often occur in a shoulder, hip, or lower areas of the legs and arms or, less commonly, in a vital organ or other tissue location that may be in virtually any part of the body.<unk>  tumors tend to recur at the site where they are surgically removed, to metastasize to other tissues, and to have poor outcomes. Surgical resection of the primary or recurrent tumor with or without adjuvant radiation therapy has been the mainstay treatment for<unk> . This treatment is often employed in order to achieve control of the tumor's local injurious effects. The sensitivity of<unk>  tumors to various chemotherapy regimens has been very limited. The prognosis of<unk>  is guarded because surgery with or without radiation therapy and chemotherapy frequently does not stop, or only stops for a short time, the progression of this disease.
Sclerosing epithelioid fibrosarcoma
Angiomyofibroblastoma
Perivascular epithelioid cell tumour
Low-grade fibromyxoid sarcoma
Lymphoepithelioma-like carcinoma
Multinucleate cell angiohistiocytoma
Undifferentiated pleomorphic sarcoma
Plexiform angiomyxoid myofibroblastic tumor