<unk> , also known as<unk>  ataxia, is a progressive neurological disorder that causes a variety of medical problems. Initially symptoms present as periodic attacks of abnormal eye movements but may intensify to longer-lasting motor incapacity. The disorder has been localized to the vestibulocerebellum, specifically the flocculonodular lobe. Symptoms of<unk>  may appear in early childhood but the full onset of neurological symptoms including nystagmus (involuntary eye movement), ataxia (loss of voluntary muscle coordination), and tinnitus (perception of sound in the absence of external stimulation) does not occur until early adulthood. To date,<unk>  has only been identified in three families but has affected multiple generations within them. Based on the familial pedigrees it has been characterized as an autosomal dominant disorder, although the exact genetic locus has not been identified. It has been found to be genetically distinct from other seemingly similar forms of neurological syndromes such as episodic ataxia types 1 and 2. Due to its rarity, however, little is known about specific details of the pathology or long-term treatment options. There is currently no cure for<unk> , although some drug therapies have been effective in alleviating particular symptoms of the disorder. Anterior view of the cerebellum showing the flocculus and nodulus of the vestibulocerebellum.
Vestibulocerebellar syndrome
Cerebellar stroke syndrome
Lateral pontine syndrome
Occipital horn syndrome
Dejerine–Roussy syndrome
Medial pontine syndrome
Lateral medullary syndrome
Amyotrophic lateral sclerosis