A<unk> <unk>  is a form of cancer of the connective tissue surrounding<unk> s. Given its origin and behavior it is classified as a sarcoma. About half the cases are diagnosed in people with neurofibromatosis; the lifetime risk for an<unk>  in patients with neurofibromatosis type 1 is 8–13%.<unk>  with rhabdomyoblastomatous component are called<unk>  triton tumors. The first-line treatment is surgical resection with wide margins. Chemotherapy (e.g. high-dose doxorubicin) and often radiotherapy are done as adjuvant and/or neoadjuvant treatment.
Malignant peripheral nerve sheath tumor
Nerve sheath tumor
Extracranial germ cell tumor
Neuroectodermal neoplasm
Central nervous system cyst
Neurolathyrism
Vertebral hemangioma
Neuroendocrine tumor