As there is no communication between the right atrium and the right ventricle, there must be an atrial septal defect to allow blood to flow into the left cardiac chambers. Due to the lack of blood flow into the right ventricle, it will be hypoplastic. In most cases, there will also be a ventricular septal defect allowing some blood into the pulmonary circulation. Due to the lack of blood flow into the pulmonary circulation, there is poor oxygenation of blood, leading to progressively worsening cyanosis.
Tricuspid atresia
Double aortic arch
Interrupted aortic arch
Persistent truncus arteriosus
Double outlet right ventricle
Double inlet left ventricle
Situs ambiguus
Transposition of the great vessels