The cause is generally either paraneoplastic syndrome or idiopathic. In idiopathic AAG, the body's own immune system targets a receptor in the autonomic ganglia, which is part of a peripheral nerve fiber. If the AAG is paraneoplastic, they have a form of cancer, and their immune system has produced paraneoplastic antibodies in response to the cancer.
Autoimmune autonomic ganglionopathy
Primary autonomic failure
Neurogenic inflammation
Visual pathway lesions
Small fiber peripheral neuropathy
Lower motor neuron lesion
Functional neurologic disorder
Upper motor neuron lesion