A large pancreas with marked hyperglucagonemia in an adult makes the diagnosis of<unk>  very likely. The existence of pancreatic tumors makes the diagnosis even more likely. Histologically, pancreatic alpha cell hyperplasia and microadenomas suggest the diagnosis of<unk> . The final diagnosis of<unk>  requires genetic test of the glucagon receptor gene.
Mahvash disease
Dejerine–Sottas disease
Keshan disease
Yushō disease
Barakat syndrome
Satoyoshi syndrome
Sugarman syndrome
Nicolau–Balus syndrome