Treatment or management of<unk> s vary; eg see methylmalonic<unk> , propionic<unk> , isovaleric<unk> , and maple syrup urine disease. As of 1984 there were no effective treatments for all of the conditions, though treatment for some included a limited protein/high carbohydrate diet, intravenous fluids, amino acid substitution, vitamin supplementation, carnitine, induced anabolism, and in some cases, tube-feeding. As of 1993 beta-ketothiolase deficiency and other OAs were managed by trying to restore biochemical and physiologic homeostasis; common therapies included restricting diet to avoid the precursor amino acids and use of compounds to either dispose of toxic metabolites or increase enzyme activity.
Organic acidemia
Propionic acidemia
Hyperammonemia
Isovaleric acidemia
Ketoacidosis
Hyperaemia
Methemoglobinemia
Azotemia