Treatment consists of wide resection or amputation. Metastases are rare at presentation but may occur in up to 30% of patients during the disease course. Prognosis is excellent, with overall survival of 85% at 10 years, but is lower when wide surgical margins cannot be obtained. This tumor is insensitive to radiation so chemotherapy is not typically used unless the cancer has metastasized to the lungs or other organs.
Adamantinoma
Neural fibrolipoma
Hamartoma
Cylindroma
Esthesioneuroblastoma
Nesidioblastoma
Lipoblastoma
Syringoma