The uterus is normally formed during embryogenesis by the fusion of the two Müllerian ducts. If one of the ducts does not develop, only one Müllerian duct contributes to the uterine development. This uterus may or may not be connected to Müllerian structure on the opposite site if the Müllerian duct on that site undergoes some development. A<unk>  has a single cervix and vagina. Associated defects may affect the renal system, and less common, the skeleton. The condition is much less common than these other uterine malformations: arcuate uterus, septate uterus, and bicornuate uterus. While the uterus didelphys is estimated to occur in 1/3,000 women, the<unk>  appears to be even more infrequent with an estimated occurrence of about 1/4,000.
Unicornuate uterus
Bicornuate uterus
Arcuate uterus
Couvelaire uterus
T-shaped uterus
Retroverted uterus
Peritoneal inclusion cyst
Ectopic decidua