Differential diagnosis * Parkes Weber syndrome * Proteus syndrome * Macrodystrophia lipomatosa Classification There is disagreement as to how cases of KTS should be classified if there is an arteriovenous fistula present. Although several authorities have suggested that the term Parkes Weber syndrome is applied in those cases, ICD-10 currently uses the term "Klippel–Trénaunay–Weber syndrome".
Klippel–Trénaunay syndrome
Klippel–Feil syndrome
Pelger–Huët anomaly
Daentl Townsend Siegel syndrome
Wiedemann–Rautenstrauch syndrome
Prader–Willi syndrome
Langer–Giedion syndrome
Saethre–Chotzen syndrome