<unk>  is characterised by attacks of epigastric pain, which are often associated with nausea and vomiting. Symptoms may start shortly after birth but onset varies periodically, with some patients not exhibiting symptoms until adulthood. There is usually progression to chronic pancreatitis with endocrine and exocrine failure and a mortally increased risk of pancreatic cancer. Lifetime risk of cancer has been variously calculated as 35–54% to the age of 75 years and screening for early pancreatic cancer is being offered to<unk>  sufferers on a scientific basis. Some patients may choose to have their pancreas surgically removed to prevent pancreatic cancer from developing in the future. The epidemiology of<unk>  follows a similar pattern to alcohol-associated chronic pancreatitis, but there are important differences. For example,<unk>  typically has an earlier age of pancreatitis onset; although malabsorption and diabetes mellitus occur at a later stage in the disease progression.
Hereditary pancreatitis
Autoimmune pancreatitis
Chronic pancreatitis
Fibrocalculous pancreatopathy
Primary sclerosing cholangitis
Whipple's disease
Primary biliary cholangitis
Secondary sclerosing cholangitis