The treatment for<unk>  is aimed at preventing abnormal heart rhythms and reducing the risk of sudden cardiac death. It has been difficult to experimentally test potential treatments as the condition is very rare, so the evidence for treatment effectiveness comes largely from consensus opinion. In addition to treating the person identified as having the condition, screening of family members may be recommended. Implantable cardioverter-defibrillator Labelled chest X-ray of a patient with an implantable cardioverter-defibrillator. In those with<unk>  who have already experienced a life-threatening abnormal heart rhythm such as ventricular fibrillation, an implantable cardioverter-defibrillator (ICD) may be recommended to reduce the chance of sudden death. This device is implanted under the skin and can continually monitor the heart rhythm. If the device detects a dangerous heart rhythm disturbance it can deliver a small electric shock with the aim of restoring a rhythm. Implanting an ICD in someone with<unk>  who has not yet experienced a life-threatening arrhythmia is more controversial but may be considered. Medication Medication aimed at correcting the ECG abnormality – the<unk> ened QT interval – has been tried. Quinidine, a class Ia antiarrhythmic agent, has been shown to partially correct the QT interval and make the heart more resilient to artificially-induced abnormal heart rhythms, although it is still uncertain at present whether this translates to a lower risk of sudden death. Sotalol, another antiarrhythmic, may prolong the QT in some subtypes of<unk> . Other medications including beta blockers, flecainide, and amiodarone have been tried, but at present there is little evidence to support their use. Drugs can also be used to treat the less dangerous abnormal heart rhythm that is also associated with<unk>  QT – atrial fibrillation. Propafenone, a class 1c antiarrhythmic, may be helpful in those with<unk>  QT to prevent atrial fibrillation. Those who develop atrial fibrillation may also require medication to decrease blood clotting in order to reduce the risk of stroke.
Short QT syndrome
Long QT syndrome
Opitz G/BBB syndrome
Brugada syndrome
Familial atrial fibrillation
Aicardi–Goutières syndrome
Phidippides cardiomyopathy
Pacak–Zhuang syndrome