Although this data may be underestimated as a result of misdiagnosis and failure to report illnesses in fatal cases, the current estimates are fairly representative of neonates with<unk> . The United States has an estimated frequency of UCED of 1 per 25,000 live births. The international prevalence is between an estimated 1:8,000-1:44,000, varying widely by location. In order for THAN to be diagnosed, urea cycle deficiencies must be excluded, and the diagnosis must be made within 24–36 hours of birth. In 1996, one study said that there were only a confirmed 33 cases of THAN worldwide in literature. This study also admitted that at first they did not consider the possibility that the infant did not have a urea cycle deficiency. The hospital that this case occurred in did not have equipment to measure urea cycle enzymes, so they confirmed the diagnosis post mortem with an autopsy. Therefore, it is important to consider that many infants diagnosed with regular<unk> , may have actually had THAN, but the urea cycle deficiency was not excluded and therefore did not meet the criteria for diagnosis.
Transient hyperammonemia of the newborn
Permanent neonatal diabetes
Neonatal hepatitis
Hemolytic disease of the newborn
Hemolytic disease of the newborn 
Transient neonatal diabetes
Neonatal diabetes
Neonatal hypoglycemia