<unk>  is caused by bilateral<unk>  lesions in the primary auditory cortex located in the temporal lobes of the brain. The ascending auditory pathways are damaged, causing a loss of perception of sound. Inner ear functions, however, remains intact.<unk>  is most often cause by stroke, but can also result from brain injury or birth defects. More specifically, a common cause is bilateral embolic stroke to the area of Heschl's gyri.<unk>  is extremely rare, with only twelve reported cases. Each case has a distinct context and different rates of recovery. It is thought that<unk>  could be a part of a spectrum of an overall<unk>  hearing disorder. In some cases, patients with<unk>  have had recovery of some hearing function, resulting in partial auditory deficits such as auditory verbal agnosia. This syndrome might be difficult to distinguish from a bilateral temporal lesion such as described above.
Cortical deafness
Post-lingual deafness
Nonsyndromic deafness
Prelingual deafness
Childhood blindness
Optic nerve hypoplasia
Surface dyslexia
Phonological dyslexia