Although large<unk><unk> s are a congenital condition, hearing loss may not be present from birth. Age of diagnosis ranges from infancy to adulthood, and symptoms include fluctuating and sometimes progressive sensorineural hearing loss and disequilibrium. It is possible that a small portion of those with large<unk><unk> s will not exhibit auditory symptoms such as hearing loss. While this is uncommon, hearing loss can progress later in life especially after head trauma. Hearing loss can be unilateral or bilateral and can be sensorineural, conductive, or mixed.<unk>  symptoms, such as vertigo and imbalance, occur in adult patients 45% of the time.
Enlarged vestibular aqueduct
Vitreous bulge
Pellucid marginal degeneration
Optokinetic drum
Optic nerve hypoplasia
Vitreomacular adhesion
Posterior cortical atrophy
Persistent pupillary membrane