The cause of iMCD is not known and no risk factors have been identified. Genetic variants have been observed in cases of<unk><unk> ; however, no genetic variant has been validated as<unk>  causing. Unlike HHV-8-associated MCD, iMCD is not caused by uncontrolled HHV-8 infection.
Idiopathic multicentric Castleman disease
Unicentric Castleman disease
Chronic multifocal Langerhans cell histiocytosis
Follicular lymphoma
Fibrin-associated diffuse large B-cell lymphoma
HHV-8-associated MCD
AIDS-related lymphoma
Progressive nodular histiocytoma