<unk>  represents 5% of all syndromes of sex development. Estimated frequency of ovotestes is one in 83,000 births (0.0012%). The exact number of confirmed cases is uncertain, but by 1991 approximately 500 cases had been confirmed. It has also been estimated that more than 525 have been documented.
True hermaphroditism
XY gonadal dysgenesis
Gonadal dysgenesis
Androgen-induced hermaphroditism
XX gonadal dysgenesis
Pseudohermaphroditism
Müllerian agenesis
45,X/46,XY mosaicism