Since the inner ear is not directly accessible to instruments, identification is by patient report of the<unk>  and audiometric testing. Of those who present to their doctor with sensorineural hearing loss, 90% report having diminished hearing, 57% report having a plugged feeling in ear, and 49% report having ringing in ear (tinnitus). About half report vestibular (vertigo) problems. For a detailed exposition of<unk>  useful for screening, a self-assessment questionnaire was developed by the American Academy of Otolaryngology, called the Hearing Handicap Inventory for Adults (HHIA). It is a 25-question survey of subjective<unk> .
symptoms of Jervell and Lange-Nielsen syndrome
symptom of Jervell and Lange-Nielsen syndrome
symptom of Andersen–Tawil syndrome
symptom of Klippel–Feil syndrome
symptom of Maroteaux–Lamy syndrome
symptoms of Rotor syndrome
symptom of Prader–Willi syndrome
symptom of Laron syndrome