<unk>  <unk>  is a rare type of long QT syndrome associated with severe, bilateral sensorineural hearing loss. Those with<unk>  are at risk of abnormal heart rhythms called arrhythmias, which can lead to fainting, seizures, or sudden death.<unk> , like other forms of long QT syndrome, causes the cardiac muscle to take<unk> r than usual to recharge between beats. It is caused by genetic variants responsible for producing ion channels that carry transport potassium out of cells. The condition is usually diagnosed using an electrocardiogram, but genetic testing can also be used. Treatment includes lifestyle measures, beta blockers, and implantation of a defibrillator in some cases. It was first described by Anton<unk>  and Fred<unk><unk>  in 1957.
Jervell and Lange-Nielsen syndrome
Long QT syndrome
Fox–Fordyce disease
Andersen–Tawil syndrome
Laron syndrome
Cowden syndrome
Koolen–De Vries syndrome
Prader–Willi syndrome