In common with other types of Charcot–Marie–Tooth disease, neurological examination reveals decreased nerve conduction velocity and histologic features of a hypertrophic demyelinating neuropathy. Electromyography shows signs of mild neurogenic damage while nerve biopsy shows onion bulb formations; the appearance of these formations is what primarily led Gustave<unk>  and Gabrielle<unk> , the scientists who first described the disorder, to classify it as a variant of Charcot–Marie–Tooth disease. To create a working nerve, neurons, Schwann cells, and fibroblasts must work together. Molecular signals are exchanged between Schwann cells and neurons to regulate survival and differentiation of a nerve. However, these signals are disrupted in patients with the<unk> .
Roussy–Lévy syndrome
Michels Caskey syndrome
Amyloid purpura
Bogart–Bacall syndrome
Char syndrome
Flammer syndrome
Michels syndrome
Golfer's vasculitis