The outlook depends on how many and how much organs are affected. The prognosis is poor if the disease presents in a young person with many affected organs, unless a newborn with skin lesions only, when the outlook is better. The prognosis is poor if liver, spleen, lung, or bone marrow is affected. A good response to chemotherapy within the first six weeks of treatment, has been found to indicate a better prognosis. In some people the condition is life-threatening. Hence, follow-up is long-term.
Chronic multifocal Langerhans cell histiocytosis
Progressive nodular histiocytoma
Progressive nodular histiocytosis
Thymoma-associated multiorgan autoimmunity
Skin manifestations of sarcoidosis
Acrokeratoelastoidosis of Costa
AIDS-related lymphoma
Inflammatory myofibroblastic tumour