Some of the childhood management issues are similar those of 21-hydroxylase deficiency: * Replacing mineralocorticoid with fludrocortisone * Suppressing DHEA and replacing cortisol with glucocorticoid * Providing extra glucocorticoid for stress * Close monitoring and perhaps other adjunctive measures to optimize growth * Deciding whether surgical repair of virilized female genitalia is warranted However, unlike 21-hydroxylase CAH, children with<unk> -HSD CAH may be unable to produce adequate amounts of testosterone (boys) or estradiol (girls) to effect normal pubertal changes. Replacement testosterone or estrogen and progesterone can be initiated at adolescence and continued throughout adult life. Fertility may be impaired by the difficulty of providing appropriate sex hormone levels in the gonads even though the basic anatomy is present.
Congenital adrenal hyperplasia due to 3β-hydroxysteroid dehydrogenase deficiency
Congenital adrenal hyperplasia due to 21-hydroxylase deficiency
Congenital adrenal hyperplasia due to 11β-hydroxylase deficiency
Congenital adrenal hyperplasia due to 17α-hydroxylase deficiency
Lipoid congenital adrenal hyperplasia
Pituitary ACTH hypersecretion
Cortisone reductase deficiency
17β-Hydroxysteroid dehydrogenase III deficiency