text: <unk>  (also known as "Striate palmoplantar keratoderma with woolly hair and cardiomyopathy" and "Striate palmoplantar keratoderma with woolly hair and left ventricular dilated cardiomyopathy,") is a cutaneous condition inherited in an autosomal recessive fashion, and due to a defect in desmoplakin.  Striate palmoplantar keratoderma, woolly hair, and left ventricular dilated cardiomyopathy has been described in both autosomal dominant and autosomal recessive forms, but only the recessive forms have a clear association with dilated cardiomyopathy.:513  The skin disease presents as a striate palmoplantar keratoderma with some nonvolar involvement, particularly at sites of pressure or abrasion.:513
option_0: Carvajal-Huerta syndrome
option_1: Achalasia-addisonian syndrome
option_2: Bloom syndrome
option_3: Schnitzler syndrome
option_4: Peutz-Jeghers syndrome
option_5: Werner syndrome
option_6: Galloway Mowat syndrome
option_7: Mirizzi's syndrome