Papillon-Lefevre syndrome: A case report of 2 affected siblings
An 11-year-old girl, younger sibling, had mixed dentition with severe gingival inflammation, abscess formation, and deep periodontal pockets []. Severe mobility affecting most of the teeth with halitosis were present. The radiographic examination using panoramic and periapical films showed severe alveolar bone loss up to the apical third region of the roots of the permanent teeth that were present, giving them the characteristic “floating-teeth” appearance [Figures and ].\nOn lateral cephalogram, there was no evidence of intracranial calcification in both patients. Laboratory investigation was carried out, which included hematological and biochemical assessment.\nRoutine blood investigations and liver function tests were found to be within the normative range of values.