Preduodenal portal vein: a 3-case series demonstrating varied presentations in infants
A 41-day-old girl presented with jaundice and increased levels of hepatic enzymes. She was born at 37 weeks of gestation by normal vaginal delivery with a birth weight of 2,700 g. Prenatally, a cardiac anomaly with complete atrioventricular septal defect, ambiguous left atrial isomerism, and a large patent ductus arteriosus were identified. On the 7th day after birth, she underwent a correction operation for the cardiac problems with subsequent complete atrioventricular blockade. Jaundice was clinically evaluated and the presence of a choledochal cyst was suggested. During surgical exploration, a portal vein crossing the bulb of the duodenum and a dilated common bile duct was found (). There was also malrotation of intestine. Hepaticojejunostomy after complete excision of a choledochal cyst was performed followed by side-to-side duodenoduodenostomy. She was discharged at 14 days after operation without complication.