Pigmented paravenous chorioretinal atrophy with Coat's like response
A 64-year-old man of Asian origin presented to us with complains of slowly progressive defective vision left eye (OS) for five years. There was no history of suggestive of previous inflammation, trauma or nyctalopia, or family history of retinal disorder. He was a known hypertensive on regular treatment.\nHis best corrected visual acuity (BCVA) was 20/20 right eye (OD) and 20/32 OS. Anterior segment was unremarkable both eyes (OU). Central fields were normal. Fundus evaluation showed pigment clumps along the retinal veins with variable chorioretinal atrophy extending from the disc up to equator OU [Fig. and ] and intraretinal and subretinal exudation with telangiectasia along the superotemporal vein OU w(more evident clinically in OS). A clinical diagnosis of PPCRA with CLR, OU was made.\nElectroretinography (ERG) was normal OU. Fluorescein angiography showed areas of hyperfluorescence in atrophic areas in the peripapillary area and hypofluorescence corresponding to the pigment clumps along the retinal veins along with its branches with telangiectasia and exudation along superotemporal vein OU and multiple macro aneurysms with capillary nonperfusion areas OS akin to Coat's disease (CD) [Fig. -].