Midline segmental odontomaxillary dysplasia
A 19-year-old female complained of an asymptomatic expansion of the anterior maxilla in midline. At age 9, the parents had sought care from a pediatric dentist because the permanent incisors in the child's maxilla failed to erupt. The gingival tissue over the unerupted permanent incisors was described as excessive and fibrous and was removed surgically to permit permanent incisors eruption. Her family history was unremarkable.\nOn clinical examination premaxillary alveolus was markedly expanded, with several protuberances visible on the labial aspect. The degree of expansion was greater than usual at age 9. All the four permanent incisors and both canines were somewhat malpositioned with wide diastemas. The enamel of the permanent incisors was hypoplastic, appearing yellowish. The marginal gingiva especially on the buccal aspect of the anterior maxillary permanent teeth appeared somewhat thickened. No pain was elicited when the area was digitally palpated [].\nPeriapical and panoramic radiographs and CT scan revealed an ill-defined, coarse, irregular trabecular bone pattern superimposed over the anterior maxillary permanent teeth [].\nSurgical recontouring of anterior maxilla together with extraction of maxillary anterior permanent teeth was performed under general anesthesia [].\nHistologic examination revealed fragments and trabeculae of immature woven bone forming irregular pattern. Mature lamellar bone was not present []. A final diagnosis of SOD was made based on the correlation of the clinical, radiographic, and microscopic findings.\nPatient was clinically asymptomatic after 6-month follow-up and was placed on interim prosthetic rehabilitation.