Primary pulmonary rhabdomyosarcoma in children: Report of three cases with review of literature
A male child aged 3 years, presented with recurrent right-sided pneumothorax with intercostal drainage for 1 year. Mass lesion was suspected and on posterolateral thoracotomy, a whitish-yellow multiple gelatinous soft cystic masses were found which were excised completely. The following roentgenogram showed excellent lung expansion. Histopathological review was suggestive of spindle cell sarcoma and immunohistochemistry (IHC) revealed cells positive for desmin and MyoD 1, suggestive of embryonal RMS. There was no evidence of metastasis and was staged as group II according to Intergroup rhabdomyosarcoma study (IRS) group. Child had received chemotherapy as per the IRS III protocol and was disease free for 160 months.