The syndromic multiple odontogenic keratocyst in siblings: A familial study
Since the family became knowledgeable about the disease process after the first member was diagnosed and treated, his sibling, a 36-year-old woman reported to us when she noticed swelling on the right side of the jaw, which gradually increased in size. The patient had skin lesions similar to her brother on the forehead and face. The forehead also showed frontal bossing.\nOPG revealed a multilocular radiolucency in the region of 36, 37, 38 extending to the ramus of mandible. A similar radiolucency was seen on the left side in association with 46, 47, 48 involving the angle region.\nOn histopathological examination, it was diagnosed to be a case of bilateral OKCs. Marsupialization followed by enucleation of the cyst was carried out on both the sides [].\nIn 2008 and a year later in 2009, the OPG showed satisfactory healing of the lesion on both the sides []. The case is being followed-up periodically. There is no evidence of recurrence of the lesion. Regular dermatological consultations are being taken for the skin lesions, which seem to be benign at this time.