Congenital Bilateral Perislyvian Syndrome: Case Report and Review of Literature
This was a case report of a 7-year-old male child, with a history of generalized tonic-clonic seizures since 2 years, born of vagina delivery with breech presentation. The child had delayed milestones, poor phonation with drooling of saliva and mental retardation and had feeding and swallowing difficulties with protrusion and movement of the tongue moderately impaired. On examination, there was atrophy of the muscles below knee with exaggerated plantar extensor reflexes on both sides. Reflexes were brisk on both sides. And also had bisyllabal speech (normally seen in 12-month-old infants). Magnetic resonance imaging (MRI) of the brain was performed, which showed the multiple small gyri in bilateral parieto-occipital cortices []. There was thickening of the grey matter around the sylvian fissure bilaterally with irregular cortex and widening the fissures [Figures and ]. Bilateral sylvain fissures were hypoplastic and extended dorsally up to the perirolandic region. The body of lateral ventricles shows inverted appearances, typical for this condition.