Myxoid Neurothekeoma: A Rare Soft Tissue Tumor of Hand in a Male Toddler
A three-year-old boy presented with a nontender, left thumb swelling of four-week duration, without any history of trauma. Fine needle aspiration cytology of the mass revealed a few plump-to-oval spindle-shaped cells in a myxoid background. Subsequently, the lesion was surgically excised. Gross examination of the submitted specimen revealed a firm, elastic, tan-colored smooth nodule, measuring 10 × 8 × 6 mm with a solid homogeneous gray cut surface []. Histopathologic examination revealed a nonencapsulated dermal tumor, composed of multiple, closely situated medium-sized nodules with scattered spindle-shaped cells in a myxoid-rich stroma []. The tumor exhibited strong positivity for S-100 immunohistochemical stain [], and focal positivity for neuron-specific enolase (NSE). Based on the histopathologic and immunohistochemical results, the case was diagnosed as nerve sheath myxoma of classical type. The patient was followed up for 10 months with no reports of recurrence.