Angiokeratoma Circumscriptum in a Young Male
A 20-year-old male presented to our department with the history of presence of multiple eruptions on his right leg since birth. These started as reddish-brown patches and became static after having initially increased in size proportional to the patient's growth. He complained of local pain and bleeding on trivial trauma. There was neither a personal history suggestive of any bleeding disorder nor occurrence of similar lesions in the family.\nSkin examination revealed multple, linear,[] dark red to brown, hyperkeratotic, warty plaques ranging from 2 × 3 cm to 7 × 5 cm with irregular borders on the shin of the right leg. On palpation, these were non-pulsatile, tender, slightly indurated, and non-compressible. Length and circumference of the legs were equal. No bruit was heard on auscultation.\nSystemic examination revealed no abnormal findings. Routine lab investigations were normal. No bony defect was detected in X-ray of the legs. Ultrasonography revealed a linear hypodense circumscribed soft tissue mass without any relationship to the underlying bone. Doppler study did not reveal any altered blood flow.\nMicroscopic evaluation of the deep incisional biopsy specimen showed hyperkeratosis, acanthosis, and extensive papillary dermal vascular proliferation, thereby, confirming our clinical impression of AKC [Figure and ]. He was referred to and managed by reconstructive surgeon via surgical excision, followed by skin grafting [Figures and ; ].