Inflammatory Linear Verrucous Epidermal Nevus in Perineum and Vulva: A Report of Two Rare Cases
A 24-year-old male presented with a pruritic, macerated plaque mostly over left perineal region since the age of 5 years with intermittent flare-up and remission. The lesion extended from the perineal region to the scrotum and inner aspect of left thigh []. Thorough examination revealed no other abnormality anywhere in the body. Family history was not significant. Histopathology revealed hyperkeratosis with a characteristic alternating orthokeratosis, hypergranulosis with parakeratosis and agranulosis along with upperdermal lymphocytic infiltrate []. Diagnosis of ILVEN was thus made and treated with topical corticosteroid without any long term benefit.