Preduodenal portal vein: a 3-case series demonstrating varied presentations in infants
An 11-day-old neonate girl presented with severe regurgitation and cyanosis during feeding. She was born at 39 weeks of gestation by cesarean section with a birth weight of 2,730 g. Dextrocardia was identified prenatally. UGI contrast study was performed and showed severe gastroesophageal reflux with delayed passage of contrast to the small bowel. Laparotomy for the reflux was planned before correction of the cardiac problem. During exploratory surgery, we found a vascular structure crossing the duodenum along with hiatal hernia. The vascular structure was confirmed to be a portal vein (). There were also malrotation of intestine and complete situs inversus. After repair of the hiatal defect with accompanying a Nissen fundoplication, a gastroduodenosotmy was performed. The postoperative clinical course was uneventful and she was discharged after undergoing a cardiac operation at 1 month.