Syndrome In Question
A 54-year-old man reported a painless retroauricular lesion, with progressive growth\nover 40 years, and lesions on the face and scalp for two years. He had hypertension\nwithout other comorbidities, and reported past surgery on the nasal crease with a\ndiagnosis of trichoepithelioma. There were no children or family history.\nAt examination he presented: frontal-parietal alopecia; (1) a 3.5 x 3 cm multilobular\nviolaceous nodule of elastic consistency in the left retroauricular region; (2) multiple\nerythematous papules and nodules on the scalp, with elastic consistency and\ntelangiectasias (turban aspect); (3) normochromic papules on the upper and lower\neyelids; (4) a 1 x 1 cm nodule with a pearlaceous border and telangiectasias in the left\nnasal region; (5) a 2 x 2 mm papule with a pearlaceous border and telangiectasias in the\nleft nasogenian groove; (6) multiple normochromic millimetre size papules on the back\n().\nIncision biopsies performed on these lesions revealed: cylindroma (1, 2, and 6);\ntrichoepithelioma (3 and 5), and trichoblastoma (4) ( e ).