This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: vitamins, Subject name: Biochemistry
[{'content': 'Which enzyme deficiency causes tyrosinemia type 1? \nSelect and explain. \nA. Fumaryl acetoacetate hydrolase, B. Tyrosine transaminase, C. HGA oxidase, D. Tyrosinase', 'role': 'user'}, {'content': 'Answer: A \nExplanation: Fumarylacetoacetate is then hydrolyzed to fumarate and acetoacetate by a hydrolase (step 6, Fig.17.2). This results in the production of a glucogenic product (fumarate) and a ketone body (acetoacetate). Hence phenylalanine and tyrosine are paly glucogenic and paly ketogenic. Impoant Specialized Products from TyrosineRef: DM Vasudevan - Textbook of Biochemistry, 6th edition, page no: 204', 'role': 'assistant'}]