This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolic disorders, Subject name: Pediatrics
[{'content': 'All the following Lipidoses are inherited as Autosomal Recessive Except \nSelect and explain. \nA. Fabry, B. Krabbe, C. Gaucher, D. Taysachs', 'role': 'user'}, {'content': 'Answer: A \nExplanation: FABRY DISEASE This disease is an X-linked inborn error of glycosphingolipid metabolism caused by the absent or markedly deficient activity of a-galactosidase A (a-gal A).Reference: Nelson Textbook of Paediatrics; 20th edition; Chapter 86; Defects in Metabolism of Lipids', 'role': 'assistant'}]