This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolism of carbohydrate, Subject name: Biochemistry
[{'content': 'Lysosomal a1 - 4 and a1 - 6 glucosidase deficiency is seen in \nSelect and explain. \nA. Von Gierke disease, B. Cori disease, C. Pompe disease, D. Tarui disease', 'role': 'user'}, {'content': 'Answer: C \nExplanation: Type Name Enzyme Deficiency Clinical Features II Pompe disease Lysosomal a1 - 4 and a1 - 6 glucosidase (acid maltase) Accumulation of glycogen in lysosomes: juvenile onset variant, Muscle hypotonia, Death from hea failure by age 2 Adult-onset variant, muscle dystrophy Reference: Harper; 30th edition; Table: 18-2; Page no: 179', 'role': 'assistant'}]