This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Biochemistry
[{'content': 'A 5 year old boy presents with hepatomegaly, hypoglycaemia & ketosis. The diagnosis is \nSelect and explain. \nA. Mucopolysaccharidosis, B. Glycogen storage disorder, C. Lipopolysaccharidosis, D. Diabetes mellitus', 'role': 'user'}, {'content': 'Answer: B \nExplanation: Patients with type I GSD may present in the neonatal period with hypoglycemia and lactic acidosis.\n\nThese children often have doll-like faces with fat cheeks, relatively thin extremities, short stature\xa0and a protuberant abdomen that is due to massive epatomegaly; the kidneys are also enlarged, whereas the spleen\xa0 and heart are normal.\nThe biochemical hallmarks of the Type Ia GSD (von Gierke’s) disease are hypoglycemia, lactic acidosis, hyperuricemia\xa0and hyperlipidemia.', 'role': 'assistant'}]