This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Integrated QBank, Subject name: Anatomy
[{'content': 'A 6-month-old child presented with multiple episodes of seizures for past 2.5 months. The child was admitted to the ward. He had frequent episodes of hypoglycemia which precipitated the seizures. O/E, Hepatosplenomegaly Sho stature Thin extremities Doll like facies Lab findings revealed hyperuricemia, lactic acidosis, hyperlipidemias Which enzyme deficiency is responsible for this disorder? \nSelect and explain. \nA. Glucose-6-phosphatase, B. Acid maltase, C. Phosphofructokinase, D. Debranching enzyme', 'role': 'user'}, {'content': 'Answer: A \nExplanation: This is a case of type I GSD/ Von-gierke disease Autosomal recessive Deficiency of Glucose-6-phosphatase in liver Presents:- Fasting hypoglycemia Lactic acidosis Hypoglycemic seizures Hepatosplenomegaly Lab findings: - Lactic acidosis Increased uric acid levels Hyperlipidemia', 'role': 'assistant'}]