This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Proteins and Amino Acids, Subject name: Biochemistry
[{'content': 'Branched chain ketoaciduria is a defect of catabolism of all the following aminoacids except- \nSelect and explain. \nA. Leucine, B. Isoleucine, C. Valine, D. Methionine', 'role': 'user'}, {'content': "Answer: D \nExplanation: Ans. is 'd' i.e., Methionine * Branched chain ketoaciduria or Maple Syrup Urine Disease (MSUD) is caused by a defect of branched chain keto acid dehydrogenase enzyme complex (BCKD). BCKD catalyses the second step of catabolism of branched chain amino acids - Leucine, Isoleucine and Valine.", 'role': 'assistant'}]