This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Disorders of Amino acid Metabolism, Subject name: Pediatrics
[{'content': "Sapropterin is used in the treatment of \nSelect and explain. \nA. Phenylketonuria, B. Hereditary Fructose Intolerance, C. Galactosemia, D. Gaucher's disease", 'role': 'user'}, {'content': "Answer: A \nExplanation: Sapropterin, a synthetic form of tetrahydrobiopterin, which acts as a cofactor in patients with residual PAH activity, is approved by FDA to reduce phenylalanine levels in PKU. Galactosemia- Avoid milk & milk products. Hereditary Fructose Intolerance- Complete elimination of sucrose & fructose drom diet. Gaucher's disease- Enzyme replacement therapy.", 'role': 'assistant'}]