This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolic disorders, Subject name: Pediatrics
[{'content': 'All are liver glycogenosis except \nSelect and explain. \nA. Von Girke disease, B. Hers disease, C. Type III glycogenosis, D. Pompes disease', 'role': 'user'}, {'content': 'Answer: D \nExplanation: Pompe disease is a muscle glycogenoses(Type II)due to enzymatic defect of Lysosomal alpha 1,4-glucosidase(acid maltase). Von Gierke is due to defect of glucose-6-phosphatase(Type Ia).Type III glycogenoses are Cori/Forbes(IIIa-liver and muscle debrancher deficiency) & Type IIIb.Hers is Type VI glycogenoses due to enzymatic defect of liver phosphorylase. Reference:Essential pediatrics-Ghai,8th edition,page no:657', 'role': 'assistant'}]