This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Miscellaneous, Subject name: Pediatrics
[{'content': 'LEIGH disease is due to the accumulation of \nSelect and explain. \nA. Glycogen, B. Pyridoxine, C. Sphingomyelin, D. None of the above', 'role': 'user'}, {'content': "Answer: A \nExplanation: (A) Glycogen # L eigh's disease or, subacute Necrotizing Encephalopathy> Is characterized by an arrest of psychomotor development, feeding problem, seizures, extraocular palsies, and weakness with hypotonia between one and 2 years of age> The cardinal Laboratory finding is lactic Addenda> Various biochemical abnormalities have been found, all of which lie in the mitrochondrial pathway for converting pyruvate to ATP.", 'role': 'assistant'}]