This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Disorders of Amino acid Metabolism, Subject name: Pediatrics
[{'content': 'Branched chain keto acids are excreted in urine in: \nSelect and explain. \nA. Maple syrup urine disease, B. Hanup disease, C. Albinism, D. Alkaptonuria', 'role': 'user'}, {'content': 'Answer: A \nExplanation: Branched chain keto acids are excreted in urine in: Maple syrup urine disease', 'role': 'assistant'}]