This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Inborn Errors of Metabolism, Subject name: Pediatrics
[{'content': 'Oochronosis is found in: \nSelect and explain. \nA. Alkaptonuria, B. Tyrosinemia, C. Phenylketonuria, D. Homocystinuria', 'role': 'user'}, {'content': "Answer: A \nExplanation: a. Alkaptonuria(Ref: Nelson's 20/e p 636, Ghai 8/e p 652)Ochronosis (dark spot on sclera/ear cartilage) is seen in Alkaptonuria which is an autosomal recessive disorder due to deficiency of enzyme homogentisic acid oxidase.", 'role': 'assistant'}]