This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Glycogen Metabolism and Glycogen Storage, Subject name: Biochemistry
[{'content': 'Enzyme deficient is Tay-Sach disease - \nSelect and explain. \nA. Hexosaminidase-A, B. Sphingomyelinase, C. Ceramidase, D. a-galactosidase', 'role': 'user'}, {'content': "Answer: A \nExplanation: Ans. is 'a' i.e., Hexosaminidase -A DiseaseEnzyme deficiencyLipid accumulatedTay-sach diseaseHexosaminidase AGM2 gangliosideSandoff diseaseHexosaminidase BGM2 gangliosideNiemann-Pick diseaseSphingomyelinaseSphingomyelineFarber's diseaseCeramidaseAcyl-sphingosine (ceramide)Fabry's diseasea-galactosidaseGlobotrisylceramideKrabbe's diseaseb-galactosidase (Galactosylceramidase)GalactosylceramideGaucher's diseaseb-glucosidase (glucocerebrosidase)GlucosylceramideMetachromatic leukodystrophyArylsulfatase A3-Sulfogalactosylceramide", 'role': 'assistant'}]