This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Inborn Errors of Metabolism, Subject name: Pediatrics
[{'content': "An Infant presents with hepatomegaly, hypoglycemia, hyperlipidemia and acidosis. Most probable underlying diagnosis is: \nSelect and explain. \nA. Von Gierke's, B. Con's disease, C. Pompe's disease, D. All of the above", 'role': 'user'}, {'content': "Answer: A \nExplanation: a. Von Gierke's(Ref: Nelson's 20/e p 715-725, Ghai 8/e p 655-657)Presence of hepatomegaly, hypoglycemia, hyperlipidemia & acidosis, point towards Von Gierke disease.", 'role': 'assistant'}]