This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Pediatrics
[{'content': "An infant has hepatorenomegaly, hypoglycemia, hyperlipidemia, acidosis and normal structured glycogen deposition in liver. What is the diagnosis ? \nSelect and explain. \nA. Her's disease, B. Von Gierke's disease, C. Cori's disease, D. Anderson's disease", 'role': 'user'}, {'content': "Answer: B \nExplanation: Ans. is 'b' i.e., Von Gierke's disease Von-Gierke disease (Type I glvcogenosis) o It is an autosomal recessive disorder. o It is due to absent or deficient activity of glucose-6-phosphatase in Liven Kidney, Intestinal mucosa o It can be divided into two subtypes ? i) Type Ia glucose - 6 - phosphatase is defective ii) Type Ib Translocase is defective (translocase transpos glucose-6-phosphatase across microsomal membrane).", 'role': 'assistant'}]