This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Disorders of Amino acid Metabolism, Subject name: Pediatrics
[{'content': 'If the tyrosinase gene is defective, it results in: \nSelect and explain. \nA. Lack of pigmentation, B. Maple syrup urine disease, C. Phenylketonuria, D. Kidney stones', 'role': 'user'}, {'content': 'Answer: A \nExplanation: Defect in Tyrosinase leads to Albinism, which presents with hypopigmentation.', 'role': 'assistant'}]