This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Biochemistry
[{'content': 'Enzyme defective in Maple syrup urine disease is: \nSelect and explain. \nA. Tyrosinase, B. Phenylalanine hydroxylase, C. Branched chain alpha ketoacid dehydrogenase, D. Homogentisate oxidase', 'role': 'user'}, {'content': 'Answer: C \nExplanation: Enzyme deficiencies and conditionsTyrosinase is deficient in albinismPhenylalanine hydroxylase is deficient in phenylketonuriaMaple syrup urine disease is due to a defect in the enzyme branched chain alpha-keto acid dehydrogenaseHomogentisate oxidase is deficient in alkaptonuria', 'role': 'assistant'}]