This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Carbohydrates, Subject name: Biochemistry
[{'content': 'A 2-week-old neonate with complete hypotonia, convulsions, failure to thrive and metabolic acidosis. The baby has small of burnt sugar in urine. The test called DNPH test is positive. What is the enzyme deficiency in this metabolic disorder? \nSelect and explain. \nA. Isovaleryl CoA dehydrogenase, B. Dihydrolipoamide dehydrogenase, C. Branched chain keto acid dehydrogenase, D. Transacylase', 'role': 'user'}, {'content': 'Answer: C \nExplanation: Ans. C. Branched chain keto acid dehydrogenase-Identifying features are early age of presentation with failure to thrive, convulsion, hypotonia-Smell of burnt sugar or caramel odour-Positive DNPH test', 'role': 'assistant'}]