This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Carbohydrates, Subject name: Biochemistry
[{'content': "Glucose 6-phosphatase deficiency occurs in \nSelect and explain. \nA. Gaucher's disease, B. Von Gierke's disease, C. Pompe's disease, D. Hurler's disease", 'role': 'user'}, {'content': "Answer: B \nExplanation: (Von Gierke's disease) (269- U.S 3rd)GLYCOGEN-STORAGE DISEASETypeNAMEENZYME-DEFECTI* Von Gierke's disease (type I glycogenosis)Glucose-6 phosphataseII*Pompe's diseaseLysosomal a-1, 4 glucosidase (acid maltase)IIICori's disease (limit dextrinosis, Forbe's disease)Amylo a-1, 6- glucosidase (debranching enzyme)IVAnderson's disease (amylopectinosis)Glucosyl 4-6 transferase (branching enzyme)VMe Ardle's disease (type V glycogenosis)Muscle glycogen phosphorylaseVIHer's diseaseLiver glycogen phosphorylaseVIITarul's diseasePhospho fructokinase SPHINGOMYELINSCEREBROSIDES1.Niemann-Pick disease - defect in enzyme sphingomyelinase1.Gaucher's disease - due to b-glucosidase defect2.Faber's disease - defect in enzyme ceramidase2.Krabbe's disease - due to b-galactosidase enzyme defect", 'role': 'assistant'}]