This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolism of protein and amino acid, Subject name: Biochemistry
[{'content': 'Maple syrup urine disease is due accumulation of \nSelect and explain. \nA. Phenylalanine, B. Tyrosine, C. Branched chain amino acids, D. Tryptophan', 'role': 'user'}, {'content': 'Answer: C \nExplanation: Maple syrup urine disease is also called branched-chain ketonuria The basic defect is deficient decarboxylation of branched-chain ketoacids.Ref: DM Vasudevan - Textbook of Biochemistry, 7th edition, page no: 230', 'role': 'assistant'}]