This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Gynaecology & Obstetrics
[{'content': "A girl has primary amenorrhea with normal ovaries, absent internal genitalia but normal external genitalia. Most probable diagnosis?: \nSelect and explain. \nA. Mayer-Rokitansky-Kuster-Hauser syndrome, B. Turner's syndrome c., C. Noonan's, D. Androgen insensitivity syndrome", 'role': 'user'}, {'content': 'Answer: A \nExplanation: The questions says that the girl has normal ovaries which rules out.\n• Turners syndrome where streak gonads are seen\n• Noonans syndrome\n• Androgen insensitivity syndrome - gonads are testis.\nSo by exclusion our answer is Mayer-Rokitansky Kuster-Hauser Syndrome.\nMullerian agenesis or mayer-okintansky-Kuster-hauser syndrome is a congenital malformation characterized by a failure of the Mullerian ducts to develop, resulting in absent uterus and variable malformations of the vagina, while both ovaries are intact and functioning.\nOvaries are present and function normally so secondary sexual characteristics are normal. External genitalia are also normal as testosterone is absent.', 'role': 'assistant'}]