This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolism of lipid, Subject name: Biochemistry
[{'content': "Sphingomyelinase deficiency is seen in \nSelect and explain. \nA. Niemann - Pick disease, B. Farber's disease, C. Tay Sach's disease, D. Krabbe's disease", 'role': 'user'}, {'content': 'Answer: A \nExplanation: DiseaseEnzyme DeficiencyClinical SymptomsNiemann-PickdiseaseSphingomyelinaseEnlarged liver and spleen, mental retardation;fatal in early lifeRef: Harper&;s Biochemistry; 30th edition; Chapter 24; 24 Metabolism of Acylglycerols & Sphingolipids', 'role': 'assistant'}]