This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Carbohydrates, Subject name: Biochemistry
[{'content': "Beta-glucosidase is defective in which disease? \nSelect and explain. \nA. Gaucher's disease, B. Tay-Sachs disease, C. Galactosaemia, D. DM", 'role': 'user'}, {'content': "Answer: A \nExplanation: Ans. a (Gaucher's disease). (Ref: Harper, Biochemistry, 25th ed., 267)Sphingolipidoses DiseaseInheritanceEnzymeCNS involvementVisceral involvement1FabryXLRAlpha-galactosidase-+2Krabbe'sARBeta-galactosidase+(bilateral thalami)+3FarberARCeramidase+/--4GaucherARBeta-Glucosidase+/-+5MetachromaticleukodystrophyARAryl sulfatase+ (Diffuse White matter)-6Niemann-PickARSphigomyelinase++7Tay-SachsARHexosaminidase A+-8SandhoffARHexosaminidase A, B++", 'role': 'assistant'}]