This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Classification and metabolism of amino acids, Subject name: Biochemistry
[{'content': 'Tomcat urine odor is seen in: \nSelect and explain. \nA. Multiple carboxylase deficiency, B. Phenylketonuria, C. Hawkinuria, D. Maple syrup disease', 'role': 'user'}, {'content': 'Answer: A \nExplanation: MULTIPLE CARBOXLASE DEFICIENCY - BIOTIN is coenzyme in carboxylase reaction. Defects in the ability to add or remove biotin from carboxylases result in multiple carboxylase deficiency. It is autosomal recessive Developmental delay Treatment is biotin supplement Tomcat Urine odour', 'role': 'assistant'}]