This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Disorders of Amino acid Metabolism, Subject name: Pediatrics
[{'content': 'In all the following metabolic disorders, clinical features are seen due to accumulation of toxic compounds EXCEPT? \nSelect and explain. \nA. Phenylketonuria, B. Maple syrup urine disease, C. Urea cycle defects, D. Mitochondrial disorders', 'role': 'user'}, {'content': 'Answer: D \nExplanation: Clinical features are seen due to accumulation of toxic compounds in: Phenylketonuria, Maple syrup urine disease, Urea cycle defects, organic acidurias & porphyrias. Mitochondrial disorders involve defects of energy production or utilisation in various organs of body.', 'role': 'assistant'}]