What is the other name of Hallervorden-Spatz syndrome?: (A) Mitochondrial encephalomyopathy; Lactic acidosis; Stroke, (B) Pantothenate kinase - associated neurodegeneration, (C) Thiamine-responsive megaloblastic anemia syndrome, (D) Riboflavin sensitive myopathy
Answer is B. Hallervorden-Spatz syndrome : Pantothenate kinase - associated neurodegeneration Rare Autosomal recessive Excessive accumulation of iron containing pigments in brain Accumulation of N-Pantothenoyl-Cysteine and Pantetheine, leading to free radical cell damage Characterized by Parkinson like features & mental retardation