Branched chain ketoaciduria is a defect of catabolism of all the following aminoacids except-: (A) Leucine, (B) Isoleucine, (C) Valine, (D) Methionine
Answer is D. Ans. is 'd' i.e., Methionine * Branched chain ketoaciduria or Maple Syrup Urine Disease (MSUD) is caused by a defect of branched chain keto acid dehydrogenase enzyme complex (BCKD). BCKD catalyses the second step of catabolism of branched chain amino acids - Leucine, Isoleucine and Valine.