Ture about Mafucci syndrome is: (A) Multiple osteochondroma, (B) Multiple Enchondroma with Hemangioma, (C) Multiple osteochindroma with soft tissue Hemangioma, (D) Multiple Hemangioma
Answer is B. Maffucci syndrome is multiple Enchondromas assosciated with soft tissue Hemangioma and thrombophlebitis MAFUCCI&;S SYNDROME : * Maffucci syndrome is a congenital non hereditary mesodermal dysplasia characterised by multiple enchondromas with soft-tissue cavernous haemangiomas. * Imaging findings are multiple enchondromas seen associated with soft tissue swelling and phleboliths. * Enchondromas degenerate into chondrosarcomas in 15-51% of cases and soft-tissue haemangiomas to vascular sarcomas in 3-5%. Refer ohopedic pathology by Vincent PG p 401