Von Hippel Lindau is associated with all except: (A) Endo lymphatic sac tumors, (B) Hemangioendotheliomas, (C) Pheochromocytoma, (D) Islet cell tumors
Answer is B. Harrison's principles of internal medicine 17th edition *Mutation of 1 allele of VHL mutation leads to retinal angiomas,CNS hemangioblastoma,pheochromocytomas,multicentric clear cell cysts,cysts involving pancreas,liver and kidneys and adenomas of kidney<\p>