Lens subluxation in Marfan&;s syndrome?: (A) Inferolateral, (B) Inferonasal, (C) Superonasal, (D) Superotemporal
Answer is D. Marfan's syndrome: It is an autosomal dominant mesodermal dysplasia. In this condition, the lens is displaced upwards and temporally (bilaterally symmetrical). Systemic anomalies include arachnodactyly (spider fingers), long extremities, hyperextensibility of joints, high arched palate and dissecting aoic aneurysm.Ref: Khurana; 4th ed; Pg 202