Hyperammonemia type-1 is due to deficiency of: (A) Arginase, (B) Arginosuccinate lyase, (C) Arginosuccinate synthase, (D) CPS-1
Answer is D. Ans. is 'd' i.e., CPS-1 Disorders caused by genetic defects of urea cycle enzymesHyperammonemia type-I Hyperammonemia type-II Citrullinemia Argininosuccinic aciduria Argi ninemiaDefective enzymeCarbamoyl phosphate synthase-I Ornithine transcarbamoylase Argininosuccinate synthase Argininosuccinate lyase ArginaseProducts accumulatedAmmonia Ammonia Citrulline Argininosuccinate Arginine.