Feature(s) of Scheibe's syndrome is/are:: (A) Semicircular canal fistula, (B) Abnormality in bony labyrinth, (C) Dysplasia of cochlea, (D) Middle ear anaomaly
Answer is C. Answer- C. Dysplasia of cochleaIt is most common inner ear anomaly.Dysplasia is seen in the cochlea & saccule; hence also called cochleosaccular dysplasia.It is inherited as an autosomal recessive nonsyndromic trait.