Male pseudohermaphroditism is seen in: (A) 5- a redutase deficiency, (B) 21 hydroxylase deficiency, (C) 17 hydroxylase deficiency, (D) Gonadal dysgenesis
Answer is A. 5 alpha reductase conve testosterone to dihydrotestosterone,which is required for external genital devolopment in male.deficiency of it leads to development of mullerian duct into fallopian tube,Uterus and upper third of vagina. Reference : Ghai essential of pediatrics, eighth edition, p.no:538