Von Gierke&;s disease is due to the deficiency of: (A) Gluc-6 phosphatase, (B) Glue-1 phosphatase, (C) Branching enzyme, (D) Mycophosphorylase
Answer is A. Glycogen storage disease type I (GSD I) or von Gierke&;s disease, is the most common of the glycogen storage diseases. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase and has an incidence in the American population of approximately 1 in 100,000 bihs.Ref: DM Vasudevan, 7th edition, page no: 128