Sweaty feet smelling urine is seen in A characteristic feature of isovaleric acidemia is a distinctive odor of sweaty feet. This odor is caused by the buildup of a compound called isovaleric acid in affected individuals. Reference: GHAI Essential pediatrics, 8th edition: (A) Maple Syrup, (B) Gaucher, (C) Isovaleric acidemia, (D) Phenyl Ketonuria
Answer is C. A characteristic feature of isovaleric acidemia is a distinctive odor of sweaty feet. This odor is caused by the buildup of a compound called isovaleric acid in affected individuals. Reference: GHAI Essential pediatrics, 8th edition