Essential Pentosuria is due to defect in?: (A) Glycolysis, (B) HMP Shunt, (C) TCA Cycle, (D) Uronic acid pathway
Answer is D. Affected individuals excrete large amounts of L-xylulose in urine. Xylulose being a reducing sugar gives Benedict's test positive. Bial's test is positive as xylulose is a pentose Reference Harper's Illustrated Biochemistry 30th Edition Pg 205