All are seen in von hippel lindau syndrome except: (A) Renal cysts, (B) Hemangioblastoma, (C) Renal clear cell carcinoma, (D) Gastric carcinoma
Answer is D. von Hippel - Lindau (VHL) disease is an autosomal dominant cancer syndrome from mutation in tumour suppressor VHL gene located on chromosome 3p. It includes: haemangioblastoma of the cerebellum, retinal angiomas, multiple RCC (clear cell type), pheochromocytoma and cysts in different organs. Reference : page 694 Textbook of pathology Harshmohan 6th edition