Bernad-Soulier Syndrome is characterised by which of the following: (A) Defect in GPIb -IX, (B) Defect in GPIIb - III a, (C) Deficiency of dence granules, (D) Deficiency of VWF
Answer is A. Bernad-Soulier Syndrome

Inherited defect in Glycoprotein = GPIb - IX
Functional platelet defect.
Defective adhesion of platelets.