True about incontinenta pigmenti include the following except –: (A) X-linked dominant, (B) Primary skin abnormality, (C) Avascularity of peripheral retina, (D) Ocular involvement is seen in almost 100% cases and is typically unilateral
Answer is D. Ocular involvement occurs in 20-35% of cases. Involvement is assynzetrical. The two pathognomic changes are -


Retinal pigmentary changes with mottled diffuse hypopigmentation.
Abnormal peripheral retinal vessels with areas of non perfusion (a vascularity).