Maple syrup urine disease is due accumulation of: (A) Phenylalanine, (B) Tyrosine, (C) Branched chain amino acids, (D) Tryptophan
Answer is C. Maple syrup urine disease is also called branched-chain ketonuria The basic defect is deficient decarboxylation of branched-chain ketoacids.Ref: DM Vasudevan - Textbook of Biochemistry, 7th edition, page no: 230