En coup de sabre lesion is seen in ?: (A) Neonatal lupus, (B) Systemic JIA, (C) Juvenile Dermatomyosistis, (D) Juvenile Scleroderma
Answer is D. En coup de Sabre lesion is seen in juvenile localized scleroderma (morphea) It appears as an indented , veical, colorless, line of skin on the forehead. The indentation looks as though the person may have struck (coup) by a sword (sabre) This lesion involves the scalp/or face; lesion can extend into the centra; nervous system, resulting in neurologic sequelae, which are most commonly seizures and headaches. Ref: nelson textbook of pediatrics 21st edition Pgno: 1286