Muscles are not involved in which glycogen storage disease?: (A) I, (B) II, (C) III, (D) IV
Answer is A. Type 1 gluconeogenesis : von gierkes disease Enzyme defect: glucose 6 phoshatase ; organs involved : liver, kidney,intestine, Charatestic features: fasting hypoglycemia,lactic acidemia,hyperacidosis,hyperlipidemia,hyperurecemia Ref: satyanarayana 4th edition pg: 269