Which of the following statements about Von-Hippel Lindau syndrome is true: (A) Multiple tumors are rarely seen, (B) craniospinal hemangioblastomas are common, (C) Superatentorial lesions are common, (D) Tumors of Schwann cells are common
Answer is B. Harrison's principles of internal medicine 17th edition. *In VHL somatic mutation of normal allele leads to retinal angiomas, CNS hemangioblastoma,pheochromocytomas and multicentric clear cysts,hemangiomas and adenomas of kidney