Uronic acid level in urine is elevated in-: (A) Tyrosinosis, (B) Maple syrup urine disease, (C) Nieman picks disease, (D) mucopolysaccharidosis
Answer is D. Uronic acid (glucuronic acid) is one of the essential components of mucopolysaccharide (glycosaminoglycans). So, it is increased in mucopolysaccharidosis.
In mucopolysaccharidosis, glucuronic acid and iduronic acid are excreted in urine.