Which disorder of carbohydrate metabolism typically has cardiac involvement?: (A) Glycogen Storage Disease Type I (Von Gierke disease), (B) Glycogen Storage Disease Type II (Pompe disease), (C) Hereditary fructose intolerance, (D) Galactosemia
Answer is B. Pompe disease: coarse facies hepatomegaly, hypotonia progressive cardiomegaly and cardiac dysfunction ECG- sho PR, large QRS complexes.