Most common cause of death in menke's disease is-: (A) Cardiac rupture, (B) Diaphragmatic paralysis, (C) Laryngospasm, (D) Cyano-methemoglobinemia
Answer is A. Ans. is 'a' i.e., Cardiac rupture o Children with this disease often die within 5 years because of dissecting aneurysms or cardiac rupture.Menkes kinky hair syndromeo An X-1 inked metabolic disturbance of copper metabolism characterized by# Mental retardation, hypocupremia, and decreased circulating ceruloplasmin.o Caused by mutations in the copper-transporting A TP7A gene.o Children with this disease often die within 5 years because of dissecting aneurysms or cardiac rupture.