Distal and collecting duct cysts are seen in?: (A) ADPKD, (B) ARPKD, (C) Tuberous sclerosis, (D) Nephronophthisis
Answer is B. ADPKD: cysts are in coex & medulla (Hepatic cyst manifestation) ARPKD: Distal & Collecting duct cyst (Hepatic fibrosis) MC age- <1yr Protein affected- Fibrocystin(Chr. 6) Presentation- B\L Abdominal mass Hypolasia of lungs Peripoal fibrosis