About Mayer rokitansky kuster hauser syndrome: (A) Ovaries uterus fallopian tubes present, (B) Uterus absent and fallopian tubes, ovaries present, (C) Ovaries uterus fallopian tubes absent, (D) Uterus present tubes and ovaries absent
Answer is B. Mayer Rokitansky Kuster Hauser syndrome ; Mullerian Agenesis (karyotype;46XX) (Phenotype female) Vagina,Uterus,Fallopian tubes absent. Typically ovaries are normal Secondary sexual characters are well developed May be associated with urologic anomalies and Skeletal malformations Management; 1.Frank dilatation 2.Vaginoplasty (Mc Indoe operation or Williams vaginoplasty) Ref: Clinical Gynecologic Endocrinology and Infeility; Eigth Edition, Chapter 9