Development of Chondrosarcomas is related with -: (A) Maffucci syndrome, (B) Felty syndrome, (C) Ollier's disease, (D) None of the above
Answer is A. MAFUCCI&;S SYNDROME * Maffucci syndrome is a congenital non hereditary mesodermal dysplasia characterised by multiple enchondromas with soft-tissue cavernous haemangiomas. * Imaging findings are multiple enchondromas seen associated with soft tissue swelling and pliboliths. * Enchondromas degenerate into chondrosarcomas in 15-51% of cases and soft-tissue haemangiomas to vascular sarcomas in 3-5%. ref : maheswari 9th ed