Most common glycogen storage disease presenting with hypoglycemia and normal glycogen structure -: (A) Von Gierke disease, (B) Pompe's disease, (C) Me Ardle's disease, (D) Forbe's disease
Answer is A. Ans. is 'a' i.e., Von Gierke disease Liver glycogenoses |Hypoglycemia| | |HepatomegalyCirrhosis|||| |RenomegalyHypoglycemia unresponsive to glucagon/epinephrineNo renomegaly Hypoglycemia corrected by glucagon/epinephrineType IV(Anderson) (Abnormal glycogen structure)||| | | Von Gierke's disease (Type I) (Normal glycogen structure)Abnormal glycogen structure Normalglycogen structure | | Type III (Cori/Forbe/limit dextrinosis)Type VI (Hers)