Features of Peutz-Jeghers syndrome are all except: (A) Autosomal dominant, (B) Mucocutaneous pigmentation, (C) Hamaomatous polyp, (D) High risk of malignacy
Answer is D. Peutz Jeghers syndrome is an autosomal dominant defect, characterised by hamaomatous intestinal polyposis and melanotic pigmentation of lips , mouth and genitalia. It DONOT UNDERGO MALIGNANT TRANSFORMATION unless a coexistant adenoma present. Reference : Harsh Mohan textbook of pathology, 7th edition.Pg no.566