Von Gierke&;s occurs due to deficiency of: (A) Glucose-6-phosphatase, (B) Liver Phosphorylase, (C) Muscle phosphorylase, (D) Debranching enzyme
Answer is A. Glycogen storage disease type I (GSD I) or von Gierke&;s disease, is the most common of the glycogen storage disease. This genetic disease results from deficiency of the enzyme glucose-6-phosphatase and has an incidence in the American population of approximately 1 in 100,000 bihs.Ref: DM Vasudevan, 7th edition, page no: 128