This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Gynaecology & Obstetrics
Primary Amenorrhea with normal ovaries normal external genitalia and normal breasts is seen in: 
Select and explain. 
A. Mayer-Rokitanski- Kuster - Hauser Syndrome, B. Turner's syndrome, C. Androgen Insensitivity syndrome, D. Noonan syndrome
A: Mayer-Rokitanski- Kuster - Hauser Syndrome
Answer: A: Mayer-Rokitanski- Kuster - Hauser Syndrome 
Explanation: It occur due to Mullerian agenesis and is characterized by normal breast, ovary, pubic and axillary hair and absent, uterus, tubes, cervix and upper 2/3rd vagina. These patients present with primary amenorrhea. Ref: Williams Gynecology, 1st Edition, Page 368; Speroff, 7th Edition, Pages 424, 421; Textbook of Gynecology By DC Dutta, 4th Edition, Pages 405, 406; Pediatric Endocrinology : A Practical Clinical Guide By Sally Radovick, Margaret H. MacGillivray, Page 389