This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Mullerian Abnormalities, Subject name: Gynaecology & Obstetrics
Pure gonadal dysgenesis will be diagnosed in the presence of 
Select and explain. 
A. Bilateral streak gonads, B. Bilateral undescended testes in male, C. One side streak and other side normal gonad, D. One side dysgenetic testis and other side dysgenetic ovary
A: Bilateral streak gonads
Answer: A: Bilateral streak gonads 
Explanation: Pure gonadal dysgenesis is characterised by B/L streak gonads. The external phenotype is female and mullerian structures are present. Usually present with primary amenorrhea (hypergonadotropic hypogonadism)