This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Ophthalmology
A young patient presents to the ophthalmology clinic with loss of central vision. ERG is normal but EOG is abnormal. Which of the following is the most likely diagnosis? 
Select and explain. 
A. Stargardt's disease, B. Best's Vtielliform Dystrophy, C. Retinitis Pigmentosa, D. Cone-Rod Dystrophy
B: Best's Vtielliform Dystrophy
Answer: B: Best's Vtielliform Dystrophy 
Explanation: It is arare, autosomal dominant, gene on chromosome 11 (11q13). It occurs between 5 -15 years of age. Sharply reduced or absent light response in EOG and normal ERG confirms diagnosis. Ref: Ophthalmology: A Pocket Textbook Atlas - Page 356.