This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolism of protein and amino acid, Subject name: Biochemistry
In alkaptonuria the urine contains 
Select and explain. 
A. Hemogentisic acid, B. Phenylalanine, C. Ketonis, D. Acetates
A: Hemogentisic acid
Answer: A: Hemogentisic acid 
Explanation: Alkaptonuria is an autosomal recessive Condition. The metabolic defect is deficiency of homogentisate oxidase. this results in excretion of homogentisic acid in urine.Ref: DM Vasudevan - Textbook of Biochemistry for Medical Students, 7th edition, page no: 237