This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Pathology
Bernad-Soulier Syndrome is characterised by which of the following 
Select and explain. 
A. Defect in GPIb -IX, B. Defect in GPIIb - III a, C. Deficiency of dence granules, D. Deficiency of VWF
A: Defect in GPIb -IX
Answer: A: Defect in GPIb -IX 
Explanation: Bernad-Soulier Syndrome

Inherited defect in Glycoprotein = GPIb - IX
Functional platelet defect.
Defective adhesion of platelets.