This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Disorders of Amino acid Metabolism, Subject name: Pediatrics
Branched chain keto acids are excreted in urine in: 
Select and explain. 
A. Maple syrup urine disease, B. Hanup disease, C. Albinism, D. Alkaptonuria
A: Maple syrup urine disease
Answer: A: Maple syrup urine disease 
Explanation: Branched chain keto acids are excreted in urine in: Maple syrup urine disease