This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Kidney, Subject name: Pathology
Bilateral Renal cell carcinoma is seen in- 
Select and explain. 
A. Eagle Barett's syndrome, B. Beckwith Weideman syndrome, C. Von HippelLindau disease, D. Bilateral Angiomyolipoma
C: Von HippelLindau disease
Answer: C: Von HippelLindau disease 
Explanation: Ans. (c) Von Hippel Lindau disease(Ref: Robbins 9th/pg 953-955)Bilateral Renal cell carcinoma is seen in Von Hippel lindau diseaseVon Hippel-Lindau (VHL) syndrome: 50-67% of individuals with VHL (nearly all, if they live long enough) develop renal cysts & bilateral, often multiple, renal cell carcinomas.Current studies implicate the VHL gene in the development of both familial and sporadic clear cell tumors.