This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolism of carbohydrate, Subject name: Biochemistry
Enzyme deficiency in Tarui disease is 
Select and explain. 
A. Glucose-6-phosphatase, B. Muscle and erythrocyte phosphofructokinase 1, C. Lysosomal a1 - 4 and a1 - 6 glucosidase, D. Liver phosphorylase kinase
B: Muscle and erythrocyte phosphofructokinase 1
Answer: B: Muscle and erythrocyte phosphofructokinase 1 
Explanation: Type name Enzyme Deficiency Clinical Features VII Tarui disease Muscle and erythrocyte phosphofructokinase 1 Poor exercise tolerance Muscle glycogen abnormally high (2.5%-4%) Blood lactate very low after exercise Also hemolytic anemia Reference: Harper; 30th edition; Table: 18-2; Page no: 179