This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Disorders of Carbohydrate Metabolism, Subject name: Pediatrics
Which disorder of carbohydrate metabolism typically has cardiac involvement? 
Select and explain. 
A. Glycogen Storage Disease Type I (Von Gierke disease), B. Glycogen Storage Disease Type II (Pompe disease), C. Hereditary fructose intolerance, D. Galactosemia
B: Glycogen Storage Disease Type II (Pompe disease)
Answer: B: Glycogen Storage Disease Type II (Pompe disease) 
Explanation: Pompe disease: coarse facies hepatomegaly, hypotonia progressive cardiomegaly and cardiac dysfunction ECG- sho PR, large QRS complexes.