This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Carbohydrates, Subject name: Biochemistry
In hereditary fructose intolerance there is defect in: 
Select and explain. 
A. Phosphofructokinase, B. Fructose 2, 6-biphosphatase, C. Fructokinase, D. Aldolase B
D: Aldolase B
Answer: D: Aldolase B 
Explanation: Ans. D. Aldolase BDefect in hepatic fructokinase causes essential fructosuria.Defect in hepatic aldolase B causes hereditary fructose intolerance.