This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolism of carbohydrate, Subject name: Biochemistry
Branching enzyme deficiency is seen in 
Select and explain. 
A. Andersen disease, B. McArdle's syndrome, C. Cori disease, D. Von Gierke disease
A: Andersen disease
Answer: A: Andersen disease 
Explanation: Type Name Enzyme Deficiency Clinical Features IV Amylopectinosis, Andersen disease Branching enzyme Hepatosplenomegaly Accumulation of polysaccharide with few branch points Death from hea or liver failure before age 5 Reference: Harper; 30th edition; Table: 18-2; Page no: 179