This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Structure and function of protein, Subject name: Biochemistry
Boiled cabbage or rancid butter smelling urine is seen in Phenylketonuria 
Select and explain. 
A. Tyrosinemia, B. Isovaleric Acidaemia, C. Multiple carboxylase deficiency, D. Phenylketonuria
A: Tyrosinemia
Answer: A: Tyrosinemia 
Explanation: REF: Lippincott book of biochemistry 6th ed. Tyrosinaemia is an error of metabolism, inherited, in which the body cannot effectively break down the amino acid tyrosine, found in most animal and plant proteins. It is an autosomal recessive, which means two copies of an abnormal gene must be present in order for this to develop. There are three types of tyrosinemia, each with distinctive symptoms and caused by the deficiency of a different enzyme. One of the symptoms of Tyrodinaemia type 1 is an odor like cabbage or rancid butter.