This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Primary Immunodeficiency, Subject name: Pediatrics
A child with pigment dilution of skin and eyes, hemorrhagic diathesis, ceroid deposition within the reticuloendothelial system has:- 
Select and explain. 
A. Bloom syndrome, B. Hermansky pudlak syndrome, C. Alezzandrini syndrome, D. Vogt-koyanogi syndrome
B: Hermansky pudlak syndrome
Answer: B: Hermansky pudlak syndrome 
Explanation: Hermansky-Pudlak syndrome Oculocutaneous albinism Ceroid accumulation in lysosomes Prolonged bleeding time. Bloom syndrome : Erythema and telangiectasia on face after exposure to sunlight Immunodeficiency, GI malabsorption and hypogonadism are common. Alezzandrini syndrome: Deafness Vitiligo Poliosis Vogt-Koyanagi-Harada syndrome: Vitiligo associated with uveitis Dysacusia Meningoencephalitis