This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Biochemistry
A 12 year old boy rapidly develops hypoglycemia after moderate activity. On physical examination, kidney and liver are found to be enlarged. Histopathology of liver shows deposits of glycogen in an excess amount. Blood examination reveals raised ketone bodies, lactic acid and triglycerides. What is the diagnosis? 
Select and explain. 
A. Von Gierke's disease, B. Pompe's disease, C. McArdle's disease, D. Cori's disease
A: Von Gierke's disease
Answer: A: Von Gierke's disease 
Explanation: Type Ia Glycogen Storage Disease-Von Gierke’s Disease

Most common Glycogen Storage Disorder in childhood.
Autosomal recessive.

The biochemical hallmarks are:

Hypoglycemia
Lactic acidosis
Hyperlipidemia
Hyperuricemia

Clinical Presentation
Most commonly present at 3–4 months of age with:

Doll like facies with fat cheeks
Relatively thin extremities
Short stature, protuberant abdomen
Massive hepatomegaly
Kidneys are also enlarged
No splenomegaly
Plasma may be milky due to associated hypertriglyceridemia

Reference- Harper’s illustrated biochemistry. 30th edition page no: 179