This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Pediatrics
A child presents with hepatomegaly and hypoglycemia. There is no improvement in blood sugar even after administration of epinephrine. What is the likely diagnosis – 
Select and explain. 
A. Von girke's disease, B. Anderson's disease, C. Pompe's disease, D. Mc Ardle's disease
A: Von girke's disease
Answer: A: Von girke's disease 
Explanation: Amongst the given options only Von Gierke's disease presents with hepatomegaly and hypoglycemia.

"A diagnosis of type I glycogen storage disease (Von Gierke's disease) should be suspected whenever there is hepatomegaly with hypoglycemia that is unresponsive to glucagon or epinephrine".