This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Pediatrics
Maple syrup urine is due to defective decarboxylation of 
Select and explain. 
A. Branched chain amino acids, B. Sulfur containing amino acids, C. Hydroxyl amino acids, D. Unbranched chain amino acids
A: Branched chain amino acids
Answer: A: Branched chain amino acids 
Explanation: None