This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Proteins and Amino Acids, Subject name: Biochemistry
Plasma tyrosine level in Richner-Hanhart syndrome is: 
Select and explain. 
A. 1-2 mg/dL, B. 2-3 mg/dL, C. 4-5 mg/dL, D. 8-10 mg/dL
C: 4-5 mg/dL
Answer: C: 4-5 mg/dL 
Explanation: Ans. C. 4-5 mg/dLTyrosinemia Type II is due to the lack of hepatic transaminase. It is also called Richner -Hanhart syndrome. During this Plasma tyrosine level is elevated 4 to 5 mg/dl. Clinical features include mental retardation, skin lesions, infants may exhibit self-mutilation and disturbances in fine co-ordination.