This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Sexuality and intersexuality, Subject name: Gynaecology & Obstetrics
A girl has primary amenorrhea with normal ovaries, absent internal genitalia but normal external genitalia. Most probable diagnosis? 
Select and explain. 
A. Mayer-Rokitansky-Kuster-Hausers- syndrome, B. Turner's syndrome, C. Noonan's, D. Androgen insensitivity syndrome
A: Mayer-Rokitansky-Kuster-Hausers- syndrome
Answer: A: Mayer-Rokitansky-Kuster-Hausers- syndrome 
Explanation: Mayer Rokitansky Kuster Hauser's syndrome : karyotype is 46,XX Normal secondary sexual charecteristics Functional ovaries Normal hormonal profile Associated with skeletal and renal anomalies Management involves creation of a functional vagina for coital purposes and can become biological mother by surrogacy. SHAW'S TEXTBOOK OF GYNAECOLOGY,Pg no:286,15th edition