This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: miscellaneous, Subject name: Biochemistry
All are lysosomal disorders, except 
Select and explain. 
A. Gaucher's disease, B. Tay Sach's disease, C. Neimann Pick disease, D. Von Geirke's disease
D: Von Geirke's disease
Answer: D: Von Geirke's disease 
Explanation: Enzyme deficiencies of :Gaucher's disease - Beta-glucosidaseNiemann-Pick disease - SphingomyelinaseTay-Sachs disease - Hexosaminidase AGlycogen storage disease, Type l (von Gierke&;s disease)Enzyme-deficient-Glucose-6-phosphataseChromosome location-17Salient features-Hepatomegaly, cirrhosis, hypoglycemia, ketosis, hyperuricemiaRef: D M Vasudevan 7th edition Page no: 144, 430