This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Biochemistry
All of the following are excreted in urine in Maple syrup urine disease, EXCEPT: 
Select and explain. 
A. Leucine, B. Isoleucine, C. Valine, D. None of the above
D: None of the above
Answer: D: None of the above 
Explanation: As the name implies, the odor of urine in maple syrup urine disease (branched-chain ketonuria) suggests maple syrup or burnt sugar. The biochemical defect involves the -keto acid decarboxylase complex. Plasma and urinary levels of leucine, isoleucine, valine, -keto acids, and -hydroxy acids (reduced -keto acids) are elevated. Ref: Harper 28th edition, chapter 29.