This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: Metabolic disorders, Subject name: Pediatrics
Mousy odour urine is seen in 
Select and explain. 
A. Maple syrup urine, B. Phenylketonuria, C. Isovalericacidria, D. Cystinuria
B: Phenylketonuria
Answer: B: Phenylketonuria 
Explanation: Mousy order urine is seen in phenylketonuria due to the presence of excessive phenylalanine and its metabolites.Mousy body odour is also present due to the excretion of phenyl lactic acid,its metabolite through sweat. Reference:Essential pediatrics-Ghai,8th edition,page no:652.