This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: None, Subject name: Pediatrics
Which among the following is associated with thrombocytopenia? 
Select and explain. 
A. Gray platelet syndrome, B. Glanzmann thrombasthenia, C. Bernard soulier syndrome, D. Storage pool disease
C: Bernard soulier syndrome
Answer: C: Bernard soulier syndrome 
Explanation: Bernard soulier syndrome is a congenital bleeding disorder characterised by thrombocytopenia with giant platelets and prolonged bleeding time. The cause for platelet dysfunction in Bernard soulier syndrome is the severe deficiency or absence of the VWF receptor (GPIb complex) on the platelet membrane. Ref: O P Ghai, 5th Edition, Page 111; Nelson, 17th Edition, Page 1936.a