This is a real-world medical entrance exam question, please give the true answer based on the question and selection. Topic name: HAEM synth and porphyrias, Subject name: Biochemistry
Which of the following inborn error of metabolism has porphyria like clinical features? 
Select and explain. 
A. Phenylketonuria, B. Tyrosinemia type I, C. Alkaptonuria, D. Metachromatic leukodystrophy
B: Tyrosinemia type I
Answer: B: Tyrosinemia type I 
Explanation: Succinylacetone accumulates in hereditary tyrosinemia type I (fumarylacetoacetate hydrolase deficiency). Succinylacetone is structurally similar to ALA and inhibits ALA dehydratase leading to porphyria like features.